Preferred Name | Cholangiocarcinoma | |
Synonyms |
Bile duct cancer |
|
Definitions |
Cholangiocarcinoma is a primary cancer originating in the biliary epithelium i.e., the cholangiocytes, of the extrahepatic and intrahepatic biliary ducts. It is extremely invasive, develops rapidly, often metastasizes, and has a very poor prognosis. They are slow growing tumors which spread longitudinally along the bile ducts with neural, perineural and subepithelial extension. |
|
ID |
http://purl.obolibrary.org/obo/HP_0030153 |
|
database_cross_reference |
SNOMEDCT_US:70179006 MSH:D018281 UMLS:C0206698 SNOMEDCT_US:312104005 NCIT:C3262 |
|
definition |
Cholangiocarcinoma is a primary cancer originating in the biliary epithelium i.e., the cholangiocytes, of the extrahepatic and intrahepatic biliary ducts. It is extremely invasive, develops rapidly, often metastasizes, and has a very poor prognosis. They are slow growing tumors which spread longitudinally along the bile ducts with neural, perineural and subepithelial extension. |
|
has exact synonym |
Bile duct cancer |
|
label |
Cholangiocarcinoma |
|
prefixIRI |
HP:0030153 |
|
prefLabel |
Cholangiocarcinoma |
|
subClassOf |