Preferred Name |
Langerhans cell histiocytosis |
|
Synonyms |
histiocytosis X |
|
Definitions |
Group of disorders characterized by monoclonal proliferation of CD1+ histiocytes. The demonstration of the langerhans cells birbeck granules is the gold standard of the phenotype. eosinophilic granuloma makes up 60-80% of all the cases. [MeSH] |
|
ID |
http://radlex.org/RID/RID3846 |
|
Definition |
Group of disorders characterized by monoclonal proliferation of CD1+ histiocytes. The demonstration of the langerhans cells birbeck granules is the gold standard of the phenotype. eosinophilic granuloma makes up 60-80% of all the cases. [MeSH] |
|
label |
RID3846 |
|
May_Cause | ||
Preferred_name |
Langerhans cell histiocytosis |
|
prefixIRI |
RID3846 |
|
prefLabel |
Langerhans cell histiocytosis |
|
Synonym |
histiocytosis X |
|
UMLS_ID |
C0019621 |
|
subClassOf |
Create mapping