Radiology Lexicon

Last uploaded: November 20, 2020
Preferred Name

Langerhans cell histiocytosis

Synonyms

histiocytosis X

Definitions

Group of disorders characterized by monoclonal proliferation of CD1+ histiocytes. The demonstration of the langerhans cells birbeck granules is the gold standard of the phenotype. eosinophilic granuloma makes up 60-80% of all the cases. [MeSH]

ID

http://radlex.org/RID/RID3846

Definition

Group of disorders characterized by monoclonal proliferation of CD1+ histiocytes. The demonstration of the langerhans cells birbeck granules is the gold standard of the phenotype. eosinophilic granuloma makes up 60-80% of all the cases. [MeSH]

label

RID3846

May_Cause

http://radlex.org/RID/RID35277

http://radlex.org/RID/RID35225

Preferred_name

Langerhans cell histiocytosis

prefixIRI

RID3846

prefLabel

Langerhans cell histiocytosis

Synonym

histiocytosis X

UMLS_ID

C0019621

subClassOf

http://radlex.org/RID/RID3845

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http://radlex.org/RID/RID3846 MIDO SAME_URI
http://purl.obolibrary.org/obo/DOID_2571 DDSS LOOM
http://purl.obolibrary.org/obo/MONDO_0018310 MONDO LOOM
http://www.limics.org/hrdo/rdfns#pat_id_3768 HRDO LOOM
http://www.orpha.net/ORDO/Orphanet_389 ORDO LOOM
http://nanbyodata.jp/ontology/NANDO_2200031 NANDO LOOM
http://www.ebi.ac.uk/efo/EFO_1000318 EFO LOOM
rgo:08562 GAMUTS LOOM
http://purl.obolibrary.org/obo/DOID_2571 CLO LOOM
http://purl.obolibrary.org/obo/DOID_2571 DOID LOOM
http://purl.obolibrary.org/obo/NCIT_C3107 BERO LOOM
http://purl.obolibrary.org/obo/MPATH_653 MPATH LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/65399007 SNOMEDCT LOOM
http://purl.jp/bio/4/id/200906015651090958 IOBC LOOM
http://purl.bioontology.org/ontology/RCTV2/C37yB00 RCTV2 LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000641624 PDQ LOOM
http://purl.bioontology.org/ontology/MEDDRA/10069698 MEDDRA LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Langerhans_Cell_Histiocytosis CSEO LOOM
http://purl.bioontology.org/ontology/OMIM/604856 OMIM LOOM
http://www.owl-ontologies.com/unnamed.owl#RID15202 DERMLEX LOOM
http://purl.obolibrary.org/obo/MONDO_0018310 DOVES LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3107 NCIT LOOM
http://www.orpha.net/ORDO/Orphanet_389 ORDO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/110450007 SNOMEDCT LOOM
http://purl.obolibrary.org/obo/DOID_2571 DTO LOOM
http://purl.obolibrary.org/obo/DOID_2571 BAO LOOM
http://purl.obolibrary.org/obo/DOID_2571 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_2571 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_2571 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_2571 FNS-H LOOM
http://purl.bioontology.org/ontology/RCD/X20E9 RCD LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_2571 NATPRO LOOM