PMO Precision Medicine Ontology

Last uploaded: December 16, 2020
Preferred Name

CREST Syndrome

Synonyms
Definitions

A syndrome characterized by calcinosis, Raynaud's phenomeno, esophageal dysmotility, sclerodactyly and telangiectasia.

ID

http://www.phoc.org.cn/pmo/class/PMO_00038508

Database_Cross_Reference

SNOMEDCT_US:201442004

ICPC2P:A99013

ICD10AM:M34.1

SNMI:D1-10240

MTH:NOCODE

NCI:C70646

CSP:4008-0097

NDFRT:N0000003618

DRUGBANK:DB09325

NCI_NICHD:C70646

COSTAR:U000018

CCPSS:0059182

DO:DOID:0060218

MDR:10011380

DXP:U000416

ICD10:M34.1

ICD10CM:M34.1

MEDCIN:36098

RCDAE:X7051

CHV:0000020818

RCD:X7051

SNOMEDCT_US:31848007

DXP:NOCODE

SNOMEDCT_US:156453002

OMIM:181750

MSH:D017675

Definition

A syndrome characterized by calcinosis, Raynaud's phenomeno, esophageal dysmotility, sclerodactyly and telangiectasia.

label

CREST Syndrome

MCID

MC00067314

PMOID

PMO:00038508

prefixIRI

pmo:PMO_00038508

prefLabel

CREST Syndrome

Synonym

CREST - Calcinosis, Raynaud's phenomenon, sclerodactyly, oesophageal involvement, telangiectasia syndrome

crst syndrome

crest

Calcinosis, Raynaud's phenomenon, Esophageal dismobility, Sclerodactyly, Telangiectasia Syndrome

CR(E)ST syndrome

Calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia (CREST) syndrome (disorder)

CREST Syndromes

Limited Cutaneous Systemic Scleroderma

Calcinos, Raynaud, sclerodactyly, oesophageal, telangiect

CREST - Calc, Raynaud, sclerodact, oesoph, telangiect

Calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia syndrome (disorder)

CREST VARIANT OF SCLERODERMA

CREST - Calc,Rayn phen,oesoph dysf,sclerodact,telangiectasia

Calcinosis cutis, Raynaud's, esophageal dysfunction, sclerodactyly and telangiectasia

Crest

Calcinosis cutis, Raynaud's, oesophageal dysfunction, sclerodactyly and telangiectasia

Calcinosis cutis, Raynaud's, esophageal dysfunction, sclerodactyly AND telangiectasia

CREST - Calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly, telangiectasia

CREST - Calcinosis, Raynaud's phenomenon, sclerodactyly, esophageal involvement, telangiectasia syndrome

Calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia syndrome

CREST syndrome

CREST Syndrome [Disease/Finding]

CREST

Calcinosis, Raynaud's phenomenon, sclerodactyly, oesophageal dysfunction, telangiectasia syndrome (disorder)

lcSSc

CREST SYNDROME

Calcinosis cutis, Raynaud's, oesophageal dysfunction, sclerodactyly AND telangiectasia

crest syndrome

Calcinosis, Raynaud phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia (CREST) syndrome

Limited Cutaneous Systemic Sclerosis

CREST - Calc/Rayn/scl/oes/tel

Calcinos, Raynaud, sclerodactyly, esophageal, telangiect

Syndrome, CREST

Calcinosis, Raynaud's phenomenon, sclerodactyly, oesophageal dysfunction, telangiectasia syndrome

Calcinosis, Raynaud's phenomenon, sclerodactyly, esophageal dysfunction, telangiectasia syndrome

CREST - Calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia

Calc/Rayn/sclerodact/oes/telan

lSSc

Calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia (CREST) syndrome

crest syndrome (diagnosis)

CREST syndrome (disorder)

Calcinosis, Raynaud's phenomenon, oesophageal dysmotility, sclerodactyly, and telangiectasia (CREST) syndrome

Tree Number

T9.14.2.2.2.1

T9.11.1.13.4.4

T9.25.3.3.1.4

T9.14.1.6.2.1

T9.20.2.37.4

T9.4.1.3.1.4

T9.1.2.4.6.1.4

T9.20.2.27.5.1

subClassOf

http://www.phoc.org.cn/pmo/class/PMO_00036396

http://www.phoc.org.cn/pmo/class/PMO_00009131

http://www.phoc.org.cn/pmo/class/PMO_00036403

http://www.phoc.org.cn/pmo/class/PMO_00036834

http://www.phoc.org.cn/pmo/class/PMO_00039251

http://www.phoc.org.cn/pmo/class/PMO_00085520

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http://purl.obolibrary.org/obo/DOID_0060218 DOID LOOM
http://purl.obolibrary.org/obo/MONDO_0019563 MONDO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.617.812.500 RH-MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0206138 OCHV LOOM
http://www.owl-ontologies.com/unnamed.owl#RID14086 DERMLEX LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D017675 RH-MESH LOOM
http://www.limics.fr/ontologies/ontolurgences#SyndromeCREST ONTOLURGENCES LOOM
http://purl.bioontology.org/ontology/RCTV2/N001100 RCTV2 LOOM
http://purl.obolibrary.org/obo/NCIT_C70646 BERO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C18.452.174.130.204 RH-MESH LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C70646 NCIT LOOM
http://purl.bioontology.org/ontology/ICD10/M34.1 ICD10 LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#20818 OCHV LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.823.225 RH-MESH LOOM
http://purl.obolibrary.org/obo/DOID_0060218 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0060218 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0060218 FNS-H LOOM
http://purl.bioontology.org/ontology/ICPC2P/A99013 ICPC2P LOOM
http://purl.obolibrary.org/obo/MONDO_0019563 DOVES LOOM
http://purl.obolibrary.org/obo/MONDO_0019563 KTAO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/31848007 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/SNMI/D1-10240 SNMI LOOM
http://purl.jp/bio/4/id/200906009479487875 IOBC LOOM
http://purl.bioontology.org/ontology/MESH/D017675 MESH LOOM
http://www.orpha.net/ORDO/Orphanet_90290 ORDO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.300.799.801.500 RH-MESH LOOM
http://purl.bioontology.org/ontology/MEDDRA/10011380 MEDDRA LOOM
http://purl.obolibrary.org/obo/OMIT_0017982 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C06.405.117.119.500.204 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.800.784.801.500 RH-MESH LOOM
http://purl.bioontology.org/ontology/ICD10CM/M34.1 ICD10CM LOOM
http://www.limics.org/hrdo/rdfns#pat_id_12001 HRDO LOOM
http://www.gamuts.net/entity#CREST_syndrome GAMUTS LOOM
http://purl.obolibrary.org/obo/DERMO_0001906 DERMO LOOM