loading...| Preferred Name |
Pleomorphic liposarcoma |
|
| Synonyms |
PLS |
|
| Definitions |
Pleomorphic liposarcoma (PLS), the rarest subtype of liposarcoma (LS; see this term), is an aggressive, fast growing tumor located usually in the deep soft tissues of the lower and upper extremities. It is characterized by a variable number of pleomorphic lipoblasts and, in contrast to dedifferentiated liposarcoma, it lacks any association with well-differentiated liposarcoma (see these terms). |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_99969 |
|
| alternative_term |
PLS |
|
| definition |
Pleomorphic liposarcoma (PLS), the rarest subtype of liposarcoma (LS; see this term), is an aggressive, fast growing tumor located usually in the deep soft tissues of the lower and upper extremities. It is characterized by a variable number of pleomorphic lipoblasts and, in contrast to dedifferentiated liposarcoma, it lacks any association with well-differentiated liposarcoma (see these terms). |
|
| definition_citation |
Orphanet |
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=99969 |
|
| has_age_of_onset |
Adult |
|
| has_inheritance |
Not applicable |
|
| hasDbXref |
ICD-10:C49.9 UMLS:C0205825 MedDRA:10073138 |
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| label |
Pleomorphic liposarcoma |
|
| notation |
ORPHA:99969 Histopathological subtype |
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_99969 |
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| prefLabel |
Pleomorphic liposarcoma |
|
| present_in |
Europe AND has_annual_incidence_average_value : 0.05 AND has_annual_incidence_range : <1 / 1 000 000 Worldwide AND has_point_prevalence_range : Unknown |
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| treeView | ||
| subClassOf |