Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Hepatocellular carcinoma

Synonyms

HCC

Definitions

Hepatocellular carcinoma is a primary hepatic cancer derived from well-differentiated hepatocytes. It is more frequent in adults than in childhood. Symptoms are hepatic mass, abdominal pain and, in advanced stages, jaundice, cachexia and liver failure.

ID

http://www.orpha.net/ORDO/Orphanet_88673

alternative_term

HCC

definition

Hepatocellular carcinoma is a primary hepatic cancer derived from well-differentiated hepatocytes. It is more frequent in adults than in childhood. Symptoms are hepatic mass, abdominal pain and, in advanced stages, jaundice, cachexia and liver failure.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=88673

has_age_of_onset

All ages

has_inheritance

Not applicable

hasDbXref

ICD-10:C22.0

UMLS:C2239176

MeSH:D006528

OMIM:114550

ICD-11:2C12.02

MedDRA:10049010

label

Hepatocellular carcinoma

notation

ORPHA:88673

Clinical group

prefixIRI

ORDO:Orphanet_88673

prefLabel

Hepatocellular carcinoma

present_in

Belgium AND has_annual_incidence_average_value : 2.275 AND has_annual_incidence_range : 1-9 / 100 000

United States AND has_annual_incidence_average_value : 6.2 AND has_annual_incidence_range : 1-9 / 100 000

Europe AND has_point_prevalence_average_value : 15.0 AND has_point_prevalence_range : 1-5 / 10 000

Poland AND has_annual_incidence_average_value : 0.925 AND has_annual_incidence_range : 1-9 / 1 000 000

Latvia AND has_annual_incidence_average_value : 1.933 AND has_annual_incidence_range : 1-9 / 100 000

Korea, Republic of AND has_annual_incidence_average_value : 49.0 AND has_annual_incidence_range : 1-5 / 10 000

Canada AND has_annual_incidence_average_value : 5.0 AND has_annual_incidence_range : 1-9 / 100 000

Estonia AND has_annual_incidence_average_value : 1.487 AND has_annual_incidence_range : 1-9 / 100 000

Netherlands AND has_annual_incidence_average_value : 1.127 AND has_annual_incidence_range : 1-9 / 100 000

Europe AND has_annual_incidence_average_value : 3.221 AND has_annual_incidence_range : 1-9 / 100 000

Mongolia AND has_annual_incidence_average_value : 99.0 AND has_annual_incidence_range : 6-9 / 10 000

China AND has_annual_incidence_average_value : 35.0 AND has_annual_incidence_range : 1-5 / 10 000

Greece AND has_annual_incidence_average_value : 15.0 AND has_annual_incidence_range : 1-5 / 10 000

Finland AND has_annual_incidence_average_value : 3.382 AND has_annual_incidence_range : 1-9 / 100 000

Japan AND has_annual_incidence_average_value : 29.0 AND has_annual_incidence_range : 1-5 / 10 000

Italy AND has_annual_incidence_average_value : 9.266 AND has_annual_incidence_range : 1-9 / 100 000

Switzerland AND has_annual_incidence_average_value : 6.649 AND has_annual_incidence_range : 1-9 / 100 000

Bulgaria AND has_annual_incidence_average_value : 1.697 AND has_annual_incidence_range : 1-9 / 100 000

Oceania AND has_annual_incidence_average_value : 5.0 AND has_annual_incidence_range : 1-9 / 100 000

Germany AND has_annual_incidence_average_value : 5.129 AND has_annual_incidence_range : 1-9 / 100 000

Austria AND has_annual_incidence_average_value : 5.296 AND has_annual_incidence_range : 1-9 / 100 000

Africa AND has_annual_incidence_average_value : 16.0 AND has_annual_incidence_range : 1-5 / 10 000

Slovakia AND has_annual_incidence_average_value : 2.762 AND has_annual_incidence_range : 1-9 / 100 000

Portugal AND has_annual_incidence_average_value : 2.345 AND has_annual_incidence_range : 1-9 / 100 000

Norway AND has_annual_incidence_average_value : 1.627 AND has_annual_incidence_range : 1-9 / 100 000

Lithuania AND has_annual_incidence_average_value : 1.146 AND has_annual_incidence_range : 1-9 / 100 000

Czech Republic AND has_annual_incidence_average_value : 2.979 AND has_annual_incidence_range : 1-9 / 100 000

Spain AND has_annual_incidence_average_value : 5.212 AND has_annual_incidence_range : 1-9 / 100 000

France AND has_annual_incidence_average_value : 6.264 AND has_annual_incidence_range : 1-9 / 100 000

Latin America AND has_annual_incidence_average_value : 12.5 AND has_annual_incidence_range : 1-5 / 10 000

Iceland AND has_annual_incidence_average_value : 1.278 AND has_annual_incidence_range : 1-9 / 100 000

Ireland AND has_annual_incidence_average_value : 1.045 AND has_annual_incidence_range : 1-9 / 100 000

United Kingdom AND has_annual_incidence_average_value : 2.106 AND has_annual_incidence_range : 1-9 / 100 000

Croatia AND has_annual_incidence_average_value : 2.762 AND has_annual_incidence_range : 1-9 / 100 000

subClassOf

http://www.orpha.net/ORDO/Orphanet_557492

http://www.orpha.net/ORDO/Orphanet_424936

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Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/MONDO_0007256 MONDO LOOM
http://purl.obolibrary.org/obo/MONDO_0007256 OBA LOOM
http://nanbyodata.jp/ontology/NANDO_2200047 NANDO LOOM
http://purl.obolibrary.org/obo/DOID_684 DOID LOOM
http://purl.obolibrary.org/obo/DOID_684 BMONT LOOM
http://purl.obolibrary.org/obo/DOID_684 VO LOOM
http://purl.obolibrary.org/obo/MONDO_0007256 OBA LOOM
http://purl.obolibrary.org/obo/HP_0001402 HP LOOM
http://purl.obolibrary.org/obo/DOID_684 CLO LOOM
http://purl.obolibrary.org/obo/DOID_684 DOID LOOM
http://purl.obolibrary.org/obo/DOID_684 VO LOOM
http://www.ebi.ac.uk/efo/EFO_0000182 EFO LOOM
rgo:02104 GAMUTS LOOM
rgo:02104 GAMUTS LOOM
http://radlex.org/RID/RID4271 RADLEX LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Hepatocellular_Carcinoma CSEO LOOM
http://purl.obolibrary.org/obo/MONDO_0007256 GCBO LOOM
http://purl.obolibrary.org/obo/MONDO_0007256 DOVES LOOM
http://purl.obolibrary.org/obo/MPATH_357 MPATH LOOM
http://purl.obolibrary.org/obo/MPATH_357 UPHENO LOOM
http://purl.obolibrary.org/obo/MPATH_357 ZP LOOM
urn:agi-pathway:uuid-7bfe358f-42c1-477f-b4b7-f6ef12486abd BPT LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_684 NATPRO LOOM
https://github.com/sap218/coid/blob/master/coid.owl#COID_00986 COID LOOM
http://purl.bioontology.org/ontology/OMIM/114550 OMIM LOOM
http://www.semanticweb.org/david/ontologies/2013/0/pathLex.owl#1.3.6.1.4.1.19376.1.8.2.1.898 PATHLEX LOOM
http://scai.fraunhofer.de/CSEO#Hepatocellular_Carcinoma CSEO LOOM
http://www.limics.org/hrdo/rdfns#pat_id_11824 HRDO LOOM
http://purl.bioontology.org/ontology/RCD/B1503 RCD LOOM
http://purl.obolibrary.org/obo/NCIT_C3099 BERO LOOM
http://purl.obolibrary.org/obo/HP_0001402 HP LOOM
http://purl.obolibrary.org/obo/HP_0001402 UPHENO LOOM
http://www.phoc.org.cn/pmo/class/PMO_00005815 PMAPP-PMO LOOM
http://purl.obolibrary.org/obo/OMIM_114550 CCO LOOM
urn:agi-folder:hepatocellular_carcinoma BPT LOOM
http://www.semanticweb.org/ontologies/2012/5/Ontology1338526551855.owl#Hepatocellular_carcinoma RPO LOOM
http://identifiers.org/omim/114550 REXO LOOM
http://identifiers.org/omim/114550 GEXO LOOM
http://identifiers.org/omim/114550 RETO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/25370001 SNOMEDCT LOOM
http://purl.obolibrary.org/obo/DOID_684 CLO LOOM
http://purl.obolibrary.org/obo/DOID_684 DTO LOOM
http://purl.obolibrary.org/obo/DOID_684 BAO LOOM
http://purl.obolibrary.org/obo/DOID_684 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_684 ODAE LOOM
http://purl.obolibrary.org/obo/DOID_684 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_684 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_684 OHMI LOOM
http://purl.obolibrary.org/obo/DOID_684 FNS-H LOOM
http://www.gamuts.net/entity#hepatocellular_carcinoma GAMUTS LOOM
http://purl.bioontology.org/ontology/CSP/2003-4684 CRISP LOOM
http://localhost/plosthes.2017-1#742 PLOSTHES LOOM
http://purl.bioontology.org/ontology/MEDDRA/10073071 MEDDRA LOOM
http://purl.bioontology.org/ontology/RCTV2/B150300 RCTV2 LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3099 NCIT LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU008946 OMIM LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C2239176 MEDLINEPLUS LOOM
http://www.gamuts.net/entity#hepatocellular_carcinoma GAMUTS REST
http://www.gamuts.net/entity#hepatocellular_carcinoma GAMUTS REST
http://www.gamuts.net/entity#hepatocellular_carcinoma GAMUTS REST