Preferred Name |
Desmoid tumor |
|
Synonyms |
Aggressive fibromatosis |
|
Definitions |
A desmoid tumor (DT) is a benign, locally invasive soft tissue tumor associated with a high recurrence rate but with no metastatic potential. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_873 |
|
alternative_term |
Aggressive fibromatosis Desmoid type fibromatosis |
|
definition |
A desmoid tumor (DT) is a benign, locally invasive soft tissue tumor associated with a high recurrence rate but with no metastatic potential. |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=873 |
|
has_age_of_onset |
Adolescent Adult |
|
has_inheritance |
Not applicable Unknown |
|
hasDbXref |
OMIM:135290 UMLS:C0079218 ICD-10:D48.1 |
|
label |
Desmoid tumor |
|
notation |
ORPHA:873 |
|
part_of | ||
prefixIRI |
ORDO:Orphanet_873 |
|
prefLabel |
Desmoid tumor |
|
present_in |
Finland AND has_annual_incidence_average_value : 0.33 AND has_annual_incidence_range : 1-9 / 1 000 000 Europe AND has_annual_incidence_average_value : 0.3 AND has_annual_incidence_range : 1-9 / 1 000 000 Worldwide AND has_point_prevalence_range : Unknown |
|
treeView | ||
subClassOf |