Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Nodular lymphocyte predominant Hodgkin lymphoma

Synonyms

NLPHL

Definitions

Nodular lymphocyte predominant Hodgkin lymphoma (NLPHL) is a rare subtype of Hodgkin lymphoma (HL; see this term) characterized histologically by malignant lymphocyte predominant (LP) cells and the absence of typical Hodgkin and Reed-Sternberg (HRS) cells.

ID

http://www.orpha.net/ORDO/Orphanet_86893

alternative_term

NLPHL

definition

Nodular lymphocyte predominant Hodgkin lymphoma (NLPHL) is a rare subtype of Hodgkin lymphoma (HL; see this term) characterized histologically by malignant lymphocyte predominant (LP) cells and the absence of typical Hodgkin and Reed-Sternberg (HRS) cells.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=86893

has_age_of_onset

All ages

has_inheritance

Unknown

hasDbXref

MedDRA:10080201

UMLS:C1334968

ICD-10:C81.0

ICD-11:2B30.0

label

Nodular lymphocyte predominant Hodgkin lymphoma

notation

ORPHA:86893

part_of

http://www.orpha.net/ORDO/Orphanet_98293

prefixIRI

ORDO:Orphanet_86893

prefLabel

Nodular lymphocyte predominant Hodgkin lymphoma

present_in

Poland AND has_annual_incidence_average_value : 0.013 AND has_annual_incidence_range : <1 / 1 000 000

Spain AND has_annual_incidence_average_value : 0.14 AND has_annual_incidence_range : 1-9 / 1 000 000

United Kingdom AND has_annual_incidence_average_value : 0.092 AND has_annual_incidence_range : <1 / 1 000 000

Slovakia AND has_annual_incidence_average_value : 0.053 AND has_annual_incidence_range : <1 / 1 000 000

Italy AND has_annual_incidence_average_value : 0.124 AND has_annual_incidence_range : 1-9 / 1 000 000

Portugal AND has_annual_incidence_average_value : 0.055 AND has_annual_incidence_range : <1 / 1 000 000

Germany AND has_annual_incidence_average_value : 0.097 AND has_annual_incidence_range : <1 / 1 000 000

Slovenia AND has_annual_incidence_average_value : 0.056 AND has_annual_incidence_range : <1 / 1 000 000

Austria AND has_annual_incidence_average_value : 0.041 AND has_annual_incidence_range : <1 / 1 000 000

Netherlands AND has_annual_incidence_average_value : 0.133 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_annual_incidence_average_value : 0.12 AND has_annual_incidence_range : 1-9 / 1 000 000

Lithuania AND has_annual_incidence_average_value : 0.008 AND has_annual_incidence_range : <1 / 1 000 000

Belgium AND has_annual_incidence_average_value : 0.128 AND has_annual_incidence_range : 1-9 / 1 000 000

Ireland AND has_annual_incidence_average_value : 0.074 AND has_annual_incidence_range : <1 / 1 000 000

Norway AND has_annual_incidence_average_value : 0.226 AND has_annual_incidence_range : 1-9 / 1 000 000

Latvia AND has_annual_incidence_average_value : 0.038 AND has_annual_incidence_range : <1 / 1 000 000

Czech Republic AND has_annual_incidence_average_value : 0.099 AND has_annual_incidence_range : <1 / 1 000 000

Worldwide AND has_point_prevalence_range : Unknown

Bulgaria AND has_annual_incidence_average_value : 0.006 AND has_annual_incidence_range : <1 / 1 000 000

Finland AND has_annual_incidence_average_value : 0.285 AND has_annual_incidence_range : 1-9 / 1 000 000

Estonia AND has_annual_incidence_average_value : 0.037 AND has_annual_incidence_range : <1 / 1 000 000

Europe AND has_annual_incidence_average_value : 0.095 AND has_annual_incidence_range : <1 / 1 000 000

Switzerland AND has_annual_incidence_average_value : 0.135 AND has_annual_incidence_range : 1-9 / 1 000 000

treeView

http://www.orpha.net/ORDO/Orphanet_98293

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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