Preferred Name |
Nodular lymphocyte predominant Hodgkin lymphoma |
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Synonyms |
NLPHL |
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Definitions |
Nodular lymphocyte predominant Hodgkin lymphoma (NLPHL) is a rare subtype of Hodgkin lymphoma (HL; see this term) characterized histologically by malignant lymphocyte predominant (LP) cells and the absence of typical Hodgkin and Reed-Sternberg (HRS) cells. |
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ID |
http://www.orpha.net/ORDO/Orphanet_86893 |
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alternative_term |
NLPHL |
|
definition |
Nodular lymphocyte predominant Hodgkin lymphoma (NLPHL) is a rare subtype of Hodgkin lymphoma (HL; see this term) characterized histologically by malignant lymphocyte predominant (LP) cells and the absence of typical Hodgkin and Reed-Sternberg (HRS) cells. |
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definition_citation |
Orphanet |
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expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=86893 |
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has_age_of_onset |
All ages |
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has_inheritance |
Unknown |
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hasDbXref |
MedDRA:10080201 UMLS:C1334968 ICD-10:C81.0 ICD-11:2B30.0 |
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label |
Nodular lymphocyte predominant Hodgkin lymphoma |
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notation |
ORPHA:86893 |
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part_of | ||
prefixIRI |
ORDO:Orphanet_86893 |
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prefLabel |
Nodular lymphocyte predominant Hodgkin lymphoma |
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present_in |
Poland AND has_annual_incidence_average_value : 0.013 AND has_annual_incidence_range : <1 / 1 000 000 Spain AND has_annual_incidence_average_value : 0.14 AND has_annual_incidence_range : 1-9 / 1 000 000 United Kingdom AND has_annual_incidence_average_value : 0.092 AND has_annual_incidence_range : <1 / 1 000 000 Slovakia AND has_annual_incidence_average_value : 0.053 AND has_annual_incidence_range : <1 / 1 000 000 Italy AND has_annual_incidence_average_value : 0.124 AND has_annual_incidence_range : 1-9 / 1 000 000 Portugal AND has_annual_incidence_average_value : 0.055 AND has_annual_incidence_range : <1 / 1 000 000 Germany AND has_annual_incidence_average_value : 0.097 AND has_annual_incidence_range : <1 / 1 000 000 Slovenia AND has_annual_incidence_average_value : 0.056 AND has_annual_incidence_range : <1 / 1 000 000 Austria AND has_annual_incidence_average_value : 0.041 AND has_annual_incidence_range : <1 / 1 000 000 Netherlands AND has_annual_incidence_average_value : 0.133 AND has_annual_incidence_range : 1-9 / 1 000 000 Worldwide AND has_annual_incidence_average_value : 0.12 AND has_annual_incidence_range : 1-9 / 1 000 000 Lithuania AND has_annual_incidence_average_value : 0.008 AND has_annual_incidence_range : <1 / 1 000 000 Belgium AND has_annual_incidence_average_value : 0.128 AND has_annual_incidence_range : 1-9 / 1 000 000 Ireland AND has_annual_incidence_average_value : 0.074 AND has_annual_incidence_range : <1 / 1 000 000 Norway AND has_annual_incidence_average_value : 0.226 AND has_annual_incidence_range : 1-9 / 1 000 000 Latvia AND has_annual_incidence_average_value : 0.038 AND has_annual_incidence_range : <1 / 1 000 000 Czech Republic AND has_annual_incidence_average_value : 0.099 AND has_annual_incidence_range : <1 / 1 000 000 Worldwide AND has_point_prevalence_range : Unknown Bulgaria AND has_annual_incidence_average_value : 0.006 AND has_annual_incidence_range : <1 / 1 000 000 Finland AND has_annual_incidence_average_value : 0.285 AND has_annual_incidence_range : 1-9 / 1 000 000 Estonia AND has_annual_incidence_average_value : 0.037 AND has_annual_incidence_range : <1 / 1 000 000 Europe AND has_annual_incidence_average_value : 0.095 AND has_annual_incidence_range : <1 / 1 000 000 Switzerland AND has_annual_incidence_average_value : 0.135 AND has_annual_incidence_range : 1-9 / 1 000 000 |
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treeView | ||
subClassOf |