loading...| Preferred Name |
Plasmacytoma |
|
| Synonyms |
Solitary plasmacytoma |
|
| Definitions |
Plasmacytoma is a localized mass of neoplastic monoclonal plasma cells that represents approximately 5% of all plasma cell neoplasms. There are two separate entities: primary plasmacytoma of the bone and extramedullary plasmacytoma of the soft tissues. Of the extramedullary plasmacytomas, 80% occur in the head and neck, usually in the upper respiratory tract. The median age at diagnosis is 50 years and the male to female ratio is 3:1. Long-term survival is possible following local radiotherapy, particularly for soft tissue presentations. |
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| ID |
http://www.orpha.net/ORDO/Orphanet_86855 |
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| alternative_term |
Solitary plasmacytoma |
|
| definition |
Plasmacytoma is a localized mass of neoplastic monoclonal plasma cells that represents approximately 5% of all plasma cell neoplasms. There are two separate entities: primary plasmacytoma of the bone and extramedullary plasmacytoma of the soft tissues. Of the extramedullary plasmacytomas, 80% occur in the head and neck, usually in the upper respiratory tract. The median age at diagnosis is 50 years and the male to female ratio is 3:1. Long-term survival is possible following local radiotherapy, particularly for soft tissue presentations. |
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| definition_citation |
Orphanet |
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=86855 |
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| has_age_of_onset |
Adult |
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| has_inheritance |
Not applicable |
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| hasDbXref |
UMLS:C0032131 ICD-10:C90.3 ICD-10:C90.2 MeSH:D010954 MedDRA:10035484 ICD-11:2A83.2 |
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| label |
Plasmacytoma |
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| notation |
ORPHA:86855 |
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_86855 |
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| prefLabel |
Plasmacytoma |
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| present_in |
United States AND has_annual_incidence_average_value : 0.34 AND has_annual_incidence_range : 1-9 / 1 000 000 Worldwide AND has_point_prevalence_range : Unknown |
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| treeView | ||
| subClassOf |