Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Acute disseminated encephalomyelitis

Synonyms

ADEM

Definitions

A demyelinating disorder of the central nervous system.

ID

http://www.orpha.net/ORDO/Orphanet_83597

alternative_term

ADEM

Acute disseminated encephalitis

definition

A demyelinating disorder of the central nervous system.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=83597

has_age_of_onset

All ages

has_inheritance

Not applicable

hasDbXref

UMLS:C0014059

ICD-10:G04.0

MedDRA:10000709

ICD-11:8A42

MeSH:D004673

label

Acute disseminated encephalomyelitis

notation

ORPHA:83597

part_of

http://www.orpha.net/ORDO/Orphanet_499047

http://www.orpha.net/ORDO/Orphanet_166490

http://www.orpha.net/ORDO/Orphanet_228145

http://www.orpha.net/ORDO/Orphanet_622014

prefixIRI

ORDO:Orphanet_83597

prefLabel

Acute disseminated encephalomyelitis

present_in

Europe AND has_annual_incidence_average_value : 0.6 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_point_prevalence_range : Unknown

treeView

http://www.orpha.net/ORDO/Orphanet_499047

http://www.orpha.net/ORDO/Orphanet_166490

http://www.orpha.net/ORDO/Orphanet_228145

http://www.orpha.net/ORDO/Orphanet_622014

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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