loading...| Preferred Name |
Desmoplastic small round cell tumor |
|
| Synonyms |
DSRCT |
|
| Definitions |
An aggressive soft tissue cancer that typically arises in serous lined surfaces of the abdominal or pelvic peritoneum, and spreads to the omentum, lymph nodes and hematogenously disseminates especially to the liver. Extraserous primary location has been reported in exceptional cases. |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_83469 |
|
| alternative_term |
DSRCT |
|
| definition |
An aggressive soft tissue cancer that typically arises in serous lined surfaces of the abdominal or pelvic peritoneum, and spreads to the omentum, lymph nodes and hematogenously disseminates especially to the liver. Extraserous primary location has been reported in exceptional cases. |
|
| definition_citation |
Orphanet |
|
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=83469 |
|
| has_age_of_onset |
Adolescent Adult |
|
| has_inheritance |
Not applicable |
|
| hasDbXref |
MedDRA:10064581 UMLS:C0281508 ICD-10:C48.2 MeSH:D058405 |
|
| label |
Desmoplastic small round cell tumor |
|
| notation |
ORPHA:83469 |
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_83469 |
|
| prefLabel |
Desmoplastic small round cell tumor |
|
| present_in |
Europe AND has_annual_incidence_range : <1 / 1 000 000 Worldwide AND has_cases/families_value : 300.0 (Case) Worldwide AND has_point_prevalence_range : Unknown |
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| treeView | ||
| subClassOf |