Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Liposarcoma

Synonyms
Definitions

Liposarcoma (LS), a type of soft tissue sarcoma, describes a group of lipomatous tumors of varying severity ranging from slow-growing to aggressive and metastatic. Liposarcomas are most often located in the lower extremities or retroperitoneum, but they can also occur in the upper extremities, neck, peritoneal cavity, spermatic cord, breast, vulva and axilla.

ID

http://www.orpha.net/ORDO/Orphanet_69078

definition

Liposarcoma (LS), a type of soft tissue sarcoma, describes a group of lipomatous tumors of varying severity ranging from slow-growing to aggressive and metastatic. Liposarcomas are most often located in the lower extremities or retroperitoneum, but they can also occur in the upper extremities, neck, peritoneal cavity, spermatic cord, breast, vulva and axilla.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=69078

has_age_of_onset

All ages

has_inheritance

Unknown

hasDbXref

OMIM:613488

ICD-11:2B59.2

ICD-11:2B59.0

ICD-11:2B59.1

ICD-11:2B59.Y

MeSH:D008080

ICD-10:C49.9

MedDRA:10024627

UMLS:C0023827

ICD-11:2B59

label

Liposarcoma

notation

ORPHA:69078

part_of

http://www.orpha.net/ORDO/Orphanet_3394

prefixIRI

ORDO:Orphanet_69078

prefLabel

Liposarcoma

present_in

Europe AND has_annual_incidence_average_value : 1.0 AND has_annual_incidence_range : 1-9 / 100 000

United States AND has_annual_incidence_average_value : 0.59 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_point_prevalence_range : Unknown

treeView

http://www.orpha.net/ORDO/Orphanet_3394

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

Delete Subject Author Type Created
No notes to display
Create mapping

Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/MONDO_0005060 MONDO LOOM
http://nanbyodata.jp/ontology/NANDO_2200065 NANDO LOOM
http://purl.obolibrary.org/obo/DOID_3382 DOID LOOM
http://purl.bioontology.org/ontology/MESH/D008080 MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.450.795.465 RH-MESH LOOM
http://purl.obolibrary.org/obo/NCIT_C3194 BERO LOOM
http://purl.jp/bio/4/id/200906045122177475 IOBC LOOM
http://purl.bioontology.org/ontology/RCD/X78Vj RCD LOOM
http://radlex.org/RID/RID4358 RADLEX LOOM
http://localhost/plosthes.2017-1#7802 PLOSTHES LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Liposarcoma CSEO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#7477 OCHV LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D008080 RH-MESH LOOM
http://purl.obolibrary.org/obo/MONDO_0005060 DOVES LOOM
http://purl.obolibrary.org/obo/MONDO_0005060 KTAO LOOM
http://purl.obolibrary.org/obo/MPATH_418 MPATH LOOM
http://purl.obolibrary.org/obo/MPATH_418 UPHENO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/254829001 SNOMEDCT LOOM
http://www.phoc.org.cn/pmo/class/PMO_00085234 PMAPP-PMO LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3194 NCIT LOOM
http://purl.obolibrary.org/obo/OMIT_0009163 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.450.550.420 RH-MESH LOOM
http://purl.obolibrary.org/obo/DERMO_0001189 DERMO LOOM
http://www.owl-ontologies.com/unnamed.owl#RID16974 DERMLEX LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0023827 OCHV LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_3382 NATPRO LOOM
http://purl.obolibrary.org/obo/HP_0012034 HP LOOM
http://purl.obolibrary.org/obo/HP_0012034 UPHENO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/1162815008 SNOMEDCT LOOM
http://www.limics.org/hrdo/rdfns#pat_id_10914 HRDO LOOM
http://purl.obolibrary.org/obo/DOID_3382 CLO LOOM
http://purl.obolibrary.org/obo/DOID_3382 DTO LOOM
http://purl.obolibrary.org/obo/DOID_3382 BAO LOOM
http://purl.obolibrary.org/obo/DOID_3382 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_3382 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_3382 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_3382 FNS-H LOOM
http://scai.fraunhofer.de/CSEO#Liposarcoma CSEO LOOM
http://www.gamuts.net/entity#liposarcoma GAMUTS LOOM
http://purl.bioontology.org/ontology/CSP/2000-7292 CRISP LOOM
http://purl.bioontology.org/ontology/MEDDRA/10024627 MEDDRA LOOM
http://www.ebi.ac.uk/efo/EFO_0000569 EFO LOOM
rgo:03258 GAMUTS LOOM
rgo:03258 GAMUTS LOOM
http://purl.obolibrary.org/obo/HP_0012034 HP LOOM
http://purl.obolibrary.org/obo/DOID_3382 CLO LOOM
http://purl.obolibrary.org/obo/DOID_3382 DOID LOOM
http://www.gamuts.net/entity#liposarcoma GAMUTS REST
http://www.gamuts.net/entity#liposarcoma GAMUTS REST
http://www.gamuts.net/entity#liposarcoma GAMUTS REST