Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Mantle cell lymphoma

Synonyms

Mantle zone lymphoma

Definitions

Mantle cell lymphoma is a rare form of malignant non-Hodgkin lymphoma (see this term) affecting B lymphocytes in the lymph nodes in a region called the ``mantle zone''.

ID

http://www.orpha.net/ORDO/Orphanet_52416

alternative_term

Mantle zone lymphoma

MCL

LCM

definition

Mantle cell lymphoma is a rare form of malignant non-Hodgkin lymphoma (see this term) affecting B lymphocytes in the lymph nodes in a region called the ``mantle zone''.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=52416

has_age_of_onset

Adult

has_inheritance

Not applicable

Multigenic/multifactorial

hasDbXref

MedDRA:10061275

UMLS:C4721414

MeSH:D020522

ICD-11:2A85.5

ICD-10:C83.1

label

Mantle cell lymphoma

notation

ORPHA:52416

part_of

http://www.orpha.net/ORDO/Orphanet_300846

prefixIRI

ORDO:Orphanet_52416

prefLabel

Mantle cell lymphoma

present_in

United States AND has_annual_incidence_average_value : 0.8 AND has_annual_incidence_range : 1-9 / 1 000 000

France AND has_annual_incidence_average_value : 1.05 AND has_annual_incidence_range : 1-9 / 100 000

Europe AND has_point_prevalence_average_value : 3.5 AND has_point_prevalence_range : 1-9 / 100 000

treeView

http://www.orpha.net/ORDO/Orphanet_300846

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/DOID_0050746 DOID LOOM
http://purl.obolibrary.org/obo/DOID_0050746 VO LOOM
http://www.ebi.ac.uk/efo/EFO_1001469 EFO LOOM
http://purl.obolibrary.org/obo/DOID_0050746 DOID LOOM
http://purl.obolibrary.org/obo/DOID_0050746 VO LOOM
http://purl.obolibrary.org/obo/MONDO_0018876 MONDO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/443487006 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/ICD9CM/200.4 ICD9CM LOOM
urn:agi-folder:mantle_cell_lymphoma BPT LOOM
http://purl.obolibrary.org/obo/MONDO_0018876 DOVES LOOM
http://www.co-ode.org/ontologies/galen#MantleCellLymphoma GALEN LOOM
http://localhost/plosthes.2017-1#3342 PLOSTHES LOOM
http://purl.bioontology.org/ontology/LNC/LA26524-1 LOINC LOOM
http://www.limics.org/hrdo/rdfns#pat_id_10693 HRDO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0334634 OCHV LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/74654000 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000042534 PDQ LOOM
http://purl.bioontology.org/ontology/ICD10CM/C83.1 ICD10CM LOOM
http://purl.obolibrary.org/obo/DOID_0050746 DTO LOOM
http://purl.obolibrary.org/obo/DOID_0050746 BAO LOOM
http://purl.obolibrary.org/obo/DOID_0050746 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0050746 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0050746 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_0050746 FNS-H LOOM
http://purl.bioontology.org/ontology/MEDDRA/10061275 MEDDRA LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C4337 NCIT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Mantle_Cell_Lymphoma CSEO LOOM
http://purl.bioontology.org/ontology/RCTV2/B62F100 RCTV2 LOOM
http://purl.obolibrary.org/obo/NCIT_C4337 BERO LOOM
urn:agi-pathway:uuid-26ce00f6-56f5-4e8c-b1e5-a4d7293b1385 BPT LOOM