Preferred Name |
Acute lymphoblastic leukemia |
|
Synonyms |
Precursor lymphoid neoplasm |
|
Definitions |
A rare disease characterized by malignant proliferation of lymphoid cells blocked at an early stage of differentiation and accounts for 75% of all cases of childhood leukaemia. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_513 |
|
alternative_term |
Precursor lymphoid neoplasm Acute lymphoblastic leukemia/lymphoma ALL Acute lymphocytic leukemia |
|
definition |
A rare disease characterized by malignant proliferation of lymphoid cells blocked at an early stage of differentiation and accounts for 75% of all cases of childhood leukaemia. |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=513 |
|
has_age_of_onset |
All ages |
|
hasDbXref |
ICD-10:C91.0 MeSH:D054198 OMIM:247640 UMLS:C1961102 OMIM:613067 OMIM:613065 |
|
label |
Acute lymphoblastic leukemia |
|
notation |
Clinical group ORPHA:513 |
|
prefixIRI |
ORDO:Orphanet_513 |
|
prefLabel |
Acute lymphoblastic leukemia |
|
present_in |
Europe AND has_annual_incidence_average_value : 2.75 AND has_annual_incidence_range : 1-9 / 100 000 United States AND has_lifetime_prevalence_average_value : 22.0 AND has_lifetime_prevalence_range : 1-5 / 10 000 United States AND has_annual_incidence_average_value : 1.6 AND has_annual_incidence_range : 1-9 / 100 000 France AND has_annual_incidence_average_value : 1.3 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_point_prevalence_average_value : 11.0 AND has_point_prevalence_range : 1-5 / 10 000 |
|
subClassOf |