Orphanet Rare Disease Ontology

Last uploaded: July 3, 2024
Preferred Name

Polyarticular juvenile idiopathic arthritis
Synonyms

Polyarticular JIA

Juvenile polyarticular arthritis

Juvenile polyarthritis

Definitions

A rare type of juvenile idiopathic arthritis characterized by arthritis with an onset prior to the age of 16 years persisting for longer than six weeks and affecting at least five joints during the first six months of the disease. Other possible causes of joint inflammation must be excluded. Two subgroups of the disease can be distinguished, based on the presence of absence of rheumatoid factor. Both subgroups are more common in girls and may be associated with mild fever, weight loss, anemia, moderate hepatosplenomegaly, and mild growth retardation.

ID

http://www.orpha.net/ORDO/Orphanet_404580

alternative_term

Polyarticular JIA

Juvenile polyarticular arthritis

Juvenile polyarthritis

definition

A rare type of juvenile idiopathic arthritis characterized by arthritis with an onset prior to the age of 16 years persisting for longer than six weeks and affecting at least five joints during the first six months of the disease. Other possible causes of joint inflammation must be excluded. Two subgroups of the disease can be distinguished, based on the presence of absence of rheumatoid factor. Both subgroups are more common in girls and may be associated with mild fever, weight loss, anemia, moderate hepatosplenomegaly, and mild growth retardation.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=404580

hasDbXref

UMLS:C4521004

label

Polyarticular juvenile idiopathic arthritis

notation

ORPHA:404580

Clinical group

prefixIRI

ORDO:Orphanet_404580

prefLabel

Polyarticular juvenile idiopathic arthritis

subClassOf

http://www.orpha.net/ORDO/Orphanet_92

http://www.orpha.net/ORDO/Orphanet_557492

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