Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
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Preferred Name

Polyarticular juvenile idiopathic arthritis
Synonyms

Polyarticular JIA
Definitions

A rare type of juvenile idiopathic arthritis characterized by arthritis with an onset prior to the age of 16 years persisting for longer than six weeks and affecting at least five joints during the first six months of the disease. Other possible causes of joint inflammation must be excluded. Two subgroups of the disease can be distinguished, based on the presence of absence of rheumatoid factor. Both subgroups are more common in girls and may be associated with mild fever, weight loss, anemia, moderate hepatosplenomegaly, and mild growth retardation.
ID

http://www.orpha.net/ORDO/Orphanet_404580
alternative_term

Polyarticular JIA

Juvenile polyarticular arthritis

Juvenile polyarthritis
definition

A rare type of juvenile idiopathic arthritis characterized by arthritis with an onset prior to the age of 16 years persisting for longer than six weeks and affecting at least five joints during the first six months of the disease. Other possible causes of joint inflammation must be excluded. Two subgroups of the disease can be distinguished, based on the presence of absence of rheumatoid factor. Both subgroups are more common in girls and may be associated with mild fever, weight loss, anemia, moderate hepatosplenomegaly, and mild growth retardation.
definition_citation

Orphanet
expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=404580
hasDbXref

UMLS:C4521004
label

Polyarticular juvenile idiopathic arthritis
notation

ORPHA:404580

Clinical group
prefixIRI

ORDO:Orphanet_404580
prefLabel

Polyarticular juvenile idiopathic arthritis
subClassOf

http://www.orpha.net/ORDO/Orphanet_92

http://www.orpha.net/ORDO/Orphanet_557492
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