Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Juvenile idiopathic arthritis

Synonyms

Juvenile rheumatoid arthritis

Juvenile chronic arthritis

Definitions

A rare, heterogeneous group of rheumatologic diseases characterized by arthritis which has an onset before 16 years of age, persists for more than 6 weeks, and is of unknown origin.

ID

http://www.orpha.net/ORDO/Orphanet_92

alternative_term

Juvenile rheumatoid arthritis

Juvenile chronic arthritis

definition

A rare, heterogeneous group of rheumatologic diseases characterized by arthritis which has an onset before 16 years of age, persists for more than 6 weeks, and is of unknown origin.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=92

has_age_of_onset

Childhood

hasDbXref

MedDRA:10059176

MeSH:D001171

UMLS:C3495559

ICD-11:FA24

label

Juvenile idiopathic arthritis

notation

Clinical group

ORPHA:92

prefixIRI

ORDO:Orphanet_92

prefLabel

Juvenile idiopathic arthritis

present_in

United States AND has_point_prevalence_average_value : 8.9 AND has_point_prevalence_range : 1-9 / 100 000

Europe AND has_annual_incidence_average_value : 1.5 AND has_annual_incidence_range : 1-9 / 100 000

Specific population AND has_point_prevalence_average_value : 74.6 AND has_point_prevalence_range : 6-9 / 10 000

Czech Republic AND has_annual_incidence_average_value : 13.0 AND has_annual_incidence_range : 1-5 / 10 000

France AND has_point_prevalence_average_value : 4.7 AND has_point_prevalence_range : 1-9 / 100 000

Worldwide AND has_point_prevalence_average_value : 20.5 AND has_point_prevalence_range : 1-5 / 10 000

Worldwide AND has_annual_incidence_average_value : 7.8 AND has_annual_incidence_range : 1-9 / 100 000

Czech Republic AND has_point_prevalence_average_value : 21.0 AND has_point_prevalence_range : 1-5 / 10 000

subClassOf

http://www.orpha.net/ORDO/Orphanet_486955

http://www.orpha.net/ORDO/Orphanet_182231

http://www.orpha.net/ORDO/Orphanet_557492

http://www.orpha.net/ORDO/Orphanet_264704

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