Preferred Name |
scimitar syndrome |
|
Synonyms |
hypogenetic lung syndrome vena cava bronchovascular syndrome congenital venolobar syndrome Halasz syndrome mirror-image lung syndrome pulmonary venolobar syndrome |
|
Definitions |
A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung. |
|
ID |
http://purl.obolibrary.org/obo/DOID_4297 |
|
database_cross_reference |
ICD10CM:Q26.8 MESH:D012587 UMLS_CUI:C0036400 SNOMEDCT_US_2023_03_01:39905002 OMIM:106700 NCI:C85056 ORDO:185 |
|
definition |
A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung. |
|
has exact synonym |
hypogenetic lung syndrome vena cava bronchovascular syndrome congenital venolobar syndrome Halasz syndrome mirror-image lung syndrome pulmonary venolobar syndrome total anomalous pulmonary venous return |
|
has_obo_namespace |
disease_ontology |
|
id |
DOID:4297 |
|
in_subset | ||
label |
scimitar syndrome |
|
notation |
DOID:4297 |
|
prefLabel |
scimitar syndrome |
|
subClassOf |