Preferred Name |
Scleroderma, Systemic [Disease/Finding] |
|
Synonyms |
Systemic Sclerosis Sclerosis, Systemic |
|
ID |
http://purl.bioontology.org/ontology/NDFRT/N0000002701 |
|
altLabel |
Systemic Sclerosis Scleroderma, Systemic Systemic Scleroderma Sclerosis, Systemic |
|
cui |
C0036421 |
|
May be treated by |
http://purl.bioontology.org/ontology/NDFRT/N0000146558 http://purl.bioontology.org/ontology/NDFRT/N0000148434 http://purl.bioontology.org/ontology/NDFRT/N0000147767 http://purl.bioontology.org/ontology/NDFRT/N0000152247 http://purl.bioontology.org/ontology/NDFRT/N0000022025 http://purl.bioontology.org/ontology/NDFRT/N0000147093 http://purl.bioontology.org/ontology/NDFRT/N0000146744 http://purl.bioontology.org/ontology/NDFRT/N0000146559 http://purl.bioontology.org/ontology/NDFRT/N0000155587 |
|
MESH DEFINITION |
A chronic multi-system disorder of CONNECTIVE TISSUE. It is characterized by SCLEROSIS in the SKIN, the LUNGS, the HEART, the GASTROINTESTINAL TRACT, the KIDNEYS, and the MUSCULOSKELETAL SYSTEM. Other important features include diseased small BLOOD VESSELS and AUTOANTIBODIES. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: LIMITED SCLERODERMA and DIFFUSE SCLERODERMA. |
|
MESH DUI |
D012595 |
|
MeSH name |
Scleroderma, Systemic |
|
MESH UI |
M0019543 |
|
NDFRT kind |
DISEASE_KIND |
|
notation |
N0000002701 |
|
NUI |
N0000002701 |
|
prefLabel |
Scleroderma, Systemic [Disease/Finding] |
|
SNOMED CID |
89155008 |
|
tui |
T047 |
|
subClassOf |