Preferred Name

Scleroderma, Systemic [Disease/Finding]

Synonyms

Systemic Sclerosis

Sclerosis, Systemic

ID

http://purl.bioontology.org/ontology/NDFRT/N0000002701

altLabel

Systemic Sclerosis

Scleroderma, Systemic

Systemic Scleroderma

Sclerosis, Systemic

cui

C0036421

May be treated by

http://purl.bioontology.org/ontology/NDFRT/N0000146558

http://purl.bioontology.org/ontology/NDFRT/N0000148434

http://purl.bioontology.org/ontology/NDFRT/N0000147767

http://purl.bioontology.org/ontology/NDFRT/N0000152247

http://purl.bioontology.org/ontology/NDFRT/N0000022025

http://purl.bioontology.org/ontology/NDFRT/N0000147093

http://purl.bioontology.org/ontology/NDFRT/N0000146744

http://purl.bioontology.org/ontology/NDFRT/N0000146559

http://purl.bioontology.org/ontology/NDFRT/N0000155587

http://purl.bioontology.org/ontology/NDFRT/N0000148036

http://purl.bioontology.org/ontology/NDFRT/N0000152248

MESH DEFINITION

A chronic multi-system disorder of CONNECTIVE TISSUE. It is characterized by SCLEROSIS in the SKIN, the LUNGS, the HEART, the GASTROINTESTINAL TRACT, the KIDNEYS, and the MUSCULOSKELETAL SYSTEM. Other important features include diseased small BLOOD VESSELS and AUTOANTIBODIES. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: LIMITED SCLERODERMA and DIFFUSE SCLERODERMA.

MESH DUI

D012595

MeSH name

Scleroderma, Systemic

MESH UI

M0019543

NDFRT kind

DISEASE_KIND

notation

N0000002701

NUI

N0000002701

prefLabel

Scleroderma, Systemic [Disease/Finding]

SNOMED CID

89155008

tui

T047

subClassOf

http://purl.bioontology.org/ontology/NDFRT/N0000000839

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MDRGER/10078638 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10036814 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10042953 MDRGER CUI
http://purl.bioontology.org/ontology/RCD/Xa1jE RCD CUI
http://purl.bioontology.org/ontology/CSP/4008-0097 CRISP CUI
http://purl.bioontology.org/ontology/ICD9CM/710.1 ICD9CM CUI
http://purl.bioontology.org/ontology/SCTSPA/89155008 SCTSPA CUI
http://purl.bioontology.org/ontology/MEDDRA/10036814 MEDDRA CUI
http://purl.bioontology.org/ontology/MESH/D012595 MESH CUI
http://purl.bioontology.org/ontology/ICD10CM/M34.0 ICD10CM CUI
http://purl.bioontology.org/ontology/MEDDRA/10042953 MEDDRA CUI
http://purl.bioontology.org/ontology/ICD10/M34.0 ICD10 CUI
http://purl.bioontology.org/ontology/SNMI/D1-10200 SNMI CUI
http://purl.bioontology.org/ontology/MDRFRE/10036814 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10078638 MDRFRE CUI
http://purl.bioontology.org/ontology/AIR/PSS AI-RHEUM CUI
http://purl.bioontology.org/ontology/AIR/DXPSS AI-RHEUM CUI
http://purl.bioontology.org/ontology/ICPC2P/L99071 ICPC2P CUI
http://purl.bioontology.org/ontology/SNOMEDCT/89155008 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0036421 MEDLINEPLUS CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000587622 PDQ CUI
http://purl.bioontology.org/ontology/MSHFRE/D012595 MSHFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10078638 MEDDRA CUI
http://purl.bioontology.org/ontology/ICD10/M34 ICD10 CUI
http://purl.bioontology.org/ontology/ICD10/M34.9 ICD10 CUI
http://purl.bioontology.org/ontology/ICPC2P/L99028 ICPC2P CUI
http://purl.bioontology.org/ontology/ICD10CM/M34.9 ICD10CM CUI
http://purl.bioontology.org/ontology/MDRFRE/10042953 MDRFRE CUI
http://evs.nci.nih.gov/ftp1/NDF-RT/NDF-RT.owl#N0000002701 INBANCIDO LOOM
http://evs.nci.nih.gov/ftp1/NDF-RT/NDF-RT.owl#N0000002701 CIDO LOOM