Preferred Name

Persistent Fetal Circulation Syndrome [Disease/Finding]

Synonyms

Familial Persistent Pulmonary Hypertension of the Newborn

ID

http://purl.bioontology.org/ontology/NDFRT/N0000002380

altLabel

Familial Persistent Pulmonary Hypertension of the Newborn

Persistent Pulmonary Hypertension of Newborn

Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins

ACDMPV

Hypertension, Pulmonary, of Newborn, Persistent

Fetal Circulation, Persistent

Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins And Other Congenital Anomalies

Persistent Fetal Circulation Syndrome

Circulation, Persistent Fetal

Pulmonary Hypertension, Familial Persistent, of the Newborn

Misalignment of the Pulmonary Vessels

ACD-MPV

Persistent Fetal Circulation

cui

C0031190

Has contraindicated drug

http://purl.bioontology.org/ontology/NDFRT/N0000146437

http://purl.bioontology.org/ontology/NDFRT/N0000164537

http://purl.bioontology.org/ontology/NDFRT/N0000151649

http://purl.bioontology.org/ontology/NDFRT/N0000151650

http://purl.bioontology.org/ontology/NDFRT/N0000151648

http://purl.bioontology.org/ontology/NDFRT/N0000164185

http://purl.bioontology.org/ontology/NDFRT/N0000164186

http://purl.bioontology.org/ontology/NDFRT/N0000164187

http://purl.bioontology.org/ontology/NDFRT/N0000151647

http://purl.bioontology.org/ontology/NDFRT/N0000151643

May be treated by

http://purl.bioontology.org/ontology/NDFRT/N0000147093

http://purl.bioontology.org/ontology/NDFRT/N0000148036

MESH DEFINITION

A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT).

MESH DUI

D010547

MeSH name

Persistent Fetal Circulation Syndrome

MESH UI

M0016380

NDFRT kind

DISEASE_KIND

notation

N0000002380

NUI

N0000002380

prefLabel

Persistent Fetal Circulation Syndrome [Disease/Finding]

SNOMED CID

35604006

233815004

206597007

tui

T047

subClassOf

http://purl.bioontology.org/ontology/NDFRT/N0000001619

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MDRGER/10034709 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10034708 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10054726 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10053592 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10083882 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10082195 MDRGER CUI
http://purl.bioontology.org/ontology/OMIM/265380 OMIM CUI
http://purl.bioontology.org/ontology/ICD10CM/P29.3 ICD10CM CUI
http://purl.bioontology.org/ontology/ICD10CM/P29.30 ICD10CM CUI
http://purl.bioontology.org/ontology/MDRFRE/10054726 MDRFRE CUI
http://purl.bioontology.org/ontology/OMIM/MTHU046520 OMIM CUI
http://purl.bioontology.org/ontology/CSP/0723-5955 CRISP CUI
http://purl.bioontology.org/ontology/SNOMEDCT/233815004 SNOMEDCT CUI
http://purl.bioontology.org/ontology/ICD9CM/747.83 ICD9CM CUI
http://purl.bioontology.org/ontology/ICPC2P/A94023 ICPC2P CUI
http://purl.bioontology.org/ontology/MDRFRE/10053592 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10034709 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10083882 MEDDRA CUI
http://purl.bioontology.org/ontology/MSHFRE/D010547 MSHFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10053592 MEDDRA CUI
http://purl.bioontology.org/ontology/SCTSPA/233815004 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRFRE/10083882 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10034709 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRFRE/10034708 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10054726 MEDDRA CUI
http://purl.bioontology.org/ontology/SNMI/D4-30010 SNMI CUI
http://purl.bioontology.org/ontology/RCD/X2001 RCD CUI
http://purl.bioontology.org/ontology/MDRFRE/10082195 MDRFRE CUI
http://purl.bioontology.org/ontology/OMIM/MTHU070849 OMIM CUI
http://purl.bioontology.org/ontology/OMIM/601089 OMIM CUI
http://purl.bioontology.org/ontology/MESH/D010547 MESH CUI
http://purl.bioontology.org/ontology/ICD10/P29.3 ICD10 CUI
http://purl.bioontology.org/ontology/MEDDRA/10034708 MEDDRA CUI
http://purl.bioontology.org/ontology/CSP/2595-6954 CRISP CUI
http://purl.bioontology.org/ontology/MEDDRA/10082195 MEDDRA CUI