Preferred Name

Moyamoya Disease [Disease/Finding]

Synonyms

Progressive Intracranial Occlusive Arteropathy (Moyamoya)

ID

http://purl.bioontology.org/ontology/NDFRT/N0000002040

altLabel

Progressive Intracranial Occlusive Arteropathy (Moyamoya)

Moya-Moya Disease

Cerebrovascular Moyamoya Disease

Moyamoya Syndrome

Moyamoya Disease

cui

C0026654

MESH DEFINITION

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

MESH DUI

D009072

MeSH name

Moyamoya Disease

MESH UI

M0014146

NDFRT kind

DISEASE_KIND

notation

N0000002040

NUI

N0000002040

prefLabel

Moyamoya Disease [Disease/Finding]

SNOMED CID

69116000

89142007

tui

T047

subClassOf

http://purl.bioontology.org/ontology/NDFRT/N0000000471

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