Preferred Name |
Dermatomyositis [Disease/Finding] |
|
Synonyms |
Dermatomyositis |
|
ID |
http://purl.bioontology.org/ontology/NDFRT/N0000000946 |
|
altLabel |
Dermatomyositis Dermatopolymyositis Polymyositis-Dermatomyositis |
|
cui |
C0011633 |
|
May be prevented by |
http://purl.bioontology.org/ontology/NDFRT/N0000150783 http://purl.bioontology.org/ontology/NDFRT/N0000165176 http://purl.bioontology.org/ontology/NDFRT/N0000161732 http://purl.bioontology.org/ontology/NDFRT/N0000150778 http://purl.bioontology.org/ontology/NDFRT/N0000191518 http://purl.bioontology.org/ontology/NDFRT/N0000191516 http://purl.bioontology.org/ontology/NDFRT/N0000191517 http://purl.bioontology.org/ontology/NDFRT/N0000146229 http://purl.bioontology.org/ontology/NDFRT/N0000150776 http://purl.bioontology.org/ontology/NDFRT/N0000150772 http://purl.bioontology.org/ontology/NDFRT/N0000162834 http://purl.bioontology.org/ontology/NDFRT/N0000150774 http://purl.bioontology.org/ontology/NDFRT/N0000150773 http://purl.bioontology.org/ontology/NDFRT/N0000150777 http://purl.bioontology.org/ontology/NDFRT/N0000150775 http://purl.bioontology.org/ontology/NDFRT/N0000150784 |
|
May be treated by |
http://purl.bioontology.org/ontology/NDFRT/N0000146744 http://purl.bioontology.org/ontology/NDFRT/N0000151453 http://purl.bioontology.org/ontology/NDFRT/N0000146286 http://purl.bioontology.org/ontology/NDFRT/N0000155587 |
|
MESH DEFINITION |
A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6) |
|
MESH DUI |
D003882 |
|
MeSH name |
Dermatomyositis |
|
MESH UI |
M0006061 |
|
NDFRT kind |
DISEASE_KIND |
|
notation |
N0000000946 |
|
NUI |
N0000000946 |
|
prefLabel |
Dermatomyositis [Disease/Finding] |
|
SNOMED CID |
396230008 |
|
tui |
T047 |
|
subClassOf |