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National Cancer Institute Thesaurus
| Preferred Name | Letterer-Siwe Disease | |
| Synonyms |
Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis Multifocal Multisystem Langerhans Cell Histiocytosis Acute Disseminated Langerhans Cell Histiocytosis Letterer-Siwe disease Letterer-Siwe Disease |
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| Definitions |
A multifocal, multisystem form of Langerhans-cell histiocytosis. There is involvement of multiple organ systems including the bones, skin, liver, spleen, and lymph nodes. Patients are usually infants presenting with fever, hepatosplenomegaly, lymphadenopathy, bone and skin lesions, and pancytopenia. |
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| ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3160 |
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| ALT_DEFINITION |
A multifocal, multisystem form of Langerhans-cell histiocytosis. There is involvement of multiple organ systems that may include the bones, skin, liver, spleen, and lymph nodes. Patients are usually infants presenting with fever, hepatosplenomegaly, lymphadenopathy, bone and skin lesions, and pancytopenia.
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| code |
C3160
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| Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156952 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C90259 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193175 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156966 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118467 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193248 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C192842 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C126659 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118168 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C165258 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C132009 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193231 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193006 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C158520 |
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| Contributing_Source |
Cellosaurus CPTAC CTRP GDC NICHD mCode
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|
| DEFINITION |
A multifocal, multisystem form of Langerhans-cell histiocytosis. There is involvement of multiple organ systems including the bones, skin, liver, spleen, and lymph nodes. Patients are usually infants presenting with fever, hepatosplenomegaly, lymphadenopathy, bone and skin lesions, and pancytopenia.
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| Display_Name |
Letterer-Siwe Disease
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| FULL_SYN |
Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis Multifocal Multisystem Langerhans Cell Histiocytosis Acute Disseminated Langerhans Cell Histiocytosis Letterer-Siwe disease Letterer-Siwe Disease
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| ICD-O-3_Code |
9754/3
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| Is_Value_For_GDC_Property | ||
| label |
Letterer-Siwe Disease
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| Legacy Concept Name |
Letterer-Siwe_Disease
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|
| Maps_To |
Letterer-Siwe disease 9751/3
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| Neoplastic_Status |
Malignant
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| Preferred_Name |
Letterer-Siwe Disease
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| prefixIRI |
Thesaurus:C3160
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| Semantic_Type |
Neoplastic Process
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| UMLS_CUI |
C0023381
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| subClassOf |
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