Nanbyo Disease Ontology

Last uploaded: February 27, 2024
Preferred Name

肝細胞癌

Synonyms
ID

http://nanbyodata.jp/ontology/NANDO_2200047

description

本疾患は小児の肝にできる原発性悪性腫瘍と定義され、肝の腫瘍性病変の中で3割弱を占める過誤腫、血管腫、血管内皮腫、奇形腫などの良性腫瘍や、また、肝悪性腫瘍の中でも転移性腫瘍は本疾患には含めない。原発性のものは上皮性の小児肝がんと非上皮性腫瘍に分かれ、その9割以上は上皮性の小児肝がんである。上皮性の小児肝がんは小児悪性固形腫瘍の3~4%を占め、その8割以上は小児特有の肝芽腫で、一部が肝細胞癌(成人型肝癌)で、稀な腫瘍として肝内胆管癌がある。非上皮性肝悪性腫瘍としては、血管内皮腫、血管肉腫、未分化肉腫、横紋筋肉腫、悪性ラブドイド腫瘍、悪性リンパ腫などがあるがいづれも稀な腫瘍である。

closeMatch

http://purl.obolibrary.org/obo/MONDO_0007256

identifier

NANDO:2200047

label

Hepatocellular carcinoma

かんさいぼうがん

肝細胞癌

prefLabel

Hepatocellular carcinoma

seeAlso

https://www.shouman.jp/disease/details/01_05_034/

https://www.kegg.jp/dbget-bin/www_bget?ds_ja:H00048

source

https://www.shouman.jp/archives/doc/doc_01_05_034_01.pdf

告示番号

10

subClassOf

http://nanbyodata.jp/ontology/NANDO_2100006

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