Preferred Name |
primary sclerosing cholangitis |
|
Synonyms |
PSC cholangitis, primary sclerosing |
|
Definitions |
Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0013433 |
|
closeMatch | ||
database_cross_reference |
Orphanet:171 UMLS:C0566602 OMIM:613806 MedDRA:10036732 SCTID:197441003 icd11.foundation:857962451 NORD:1613 GARD:1280 DOID:0060643 |
|
definition |
Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure. |
|
exactMatch |
http://purl.obolibrary.org/obo/Orphanet_171 http://identifiers.org/snomedct/197441003 http://purl.obolibrary.org/obo/DOID_0060643 |
|
has_exact_synonym |
PSC |
|
has_related_synonym |
cholangitis, primary sclerosing |
|
id |
MONDO:0013433 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo#ordo_disease http://purl.obolibrary.org/obo/mondo#rare http://purl.obolibrary.org/obo/mondo#nord_rare |
|
label |
primary sclerosing cholangitis |
|
notation |
MONDO:0013433 |
|
prefLabel |
primary sclerosing cholangitis |
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treeView | ||
subClassOf |