loading...| Preferred Name | neurofibrosarcoma | |
| Synonyms |
neurosarcoma [obs] neurosarcoma |
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| Definitions |
A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with neurofibromatosis 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72) |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0002675 |
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| database_cross_reference |
MESH:D018319 DOID:3512 SCTID:404037002 GARD:8211 MEDGEN:104927 UMLS:C0206729 |
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| definition |
A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with neurofibromatosis 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72) |
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| has_exact_synonym |
neurosarcoma [obs] neurosarcoma |
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| id |
MONDO:0002675 |
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| in_subset | ||
| label |
neurofibrosarcoma |
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| notation |
MONDO:0002675 |
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| prefLabel |
neurofibrosarcoma |
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| skos_exactMatch |
http://linkedlifedata.com/resource/umls/id/C0206729 http://identifiers.org/mesh/D018319 |
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| treeView | ||
| subClassOf |