loading...| Preferred Name |
scimitar syndrome |
|
| Synonyms |
pulmonary venolobar syndrome |
|
| Definitions |
A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung. |
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| ID |
http://purl.obolibrary.org/obo/DOID_4297 |
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| database_cross_reference |
UMLS_CUI:C0036400 ICD10CM:Q26.8 OMIM:106700 MESH:D012587 ORDO:185 SNOMEDCT_US_2021_09_01:39905002 NCI:C85056 |
|
| definition |
A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung. |
|
| has_exact_synonym |
pulmonary venolobar syndrome total anomalous pulmonary venous return congenital venolobar syndrome hypogenetic lung syndrome vena cava bronchovascular syndrome Halasz syndrome mirror-image lung syndrome |
|
| has_obo_namespace |
disease_ontology |
|
| IAO_0000115 |
A congenital heart disease that is characterized by partial or entire anomalous curved venous drainage of the right lung to the inferior vena cava, association with variable right lung and pulmonary artery hypoplasia, dextraposition of the heart and an anomalous systemic blood supply to the ipsilateral lung. |
|
| id |
DOID:4297 |
|
| in_subset | ||
| label |
scimitar syndrome |
|
| notation |
DOID:4297 |
|
| prefLabel |
scimitar syndrome |
|
| subClassOf |