Preferred Name | Langerhans-cell histiocytosis | |
Synonyms |
Histiocytosis X Letterer-Siwe disease of lymph nodes of multiple sites Letterer-Siwe disease involving intrathoracic lymph nodes Letterer-Siwe disease of lymph nodes of inguinal region and lower limb Letterer-Siwe disease involving lymph nodes of axilla and upper limb Langerhan's cell histiocytosis Letterer-Siwe disease of spleen Letterer-Siwe disease of intrathoracic lymph nodes Letterer-Siwe disease Letterer-Siwe disease of lymph nodes of inguinal region amd/or lower limb Letterer-Siwe disease of lymph nodes of axilla and/or upper limb Letterer-Siwe disease involving lymph nodes of head, face and neck Letterer-Siwe disease involving lymph nodes of head, face, and neck Letterer-Siwe disease involving intra-abdominal lymph nodes Letterer-Siwe disease involving lymph nodes of multiple sites Langerhans cell granulomatosis Letterer-Siwe disease of lymph nodes of head, face and neck Letterer-Siwe disease of lymph nodes of head, face and/or neck Letterer-Siwe disease involving intrapelvic lymph nodes Letterer-Siwe disease of lymph nodes of axilla and upper limb Letterer-Siwe disease of intra-abdominal lymph nodes Letterer-Siwe disease of lymph nodes of inguinal region and/or lower limb Letterer-Siwe disease involving lymph nodes of inguinal region and lower limb Letterer-Siwe disease of intrapelvic lymph nodes Letterer-Siwe disease involving spleen |
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Definitions |
A histiocytosis that is characterized by clonal proliferation of Langerhans cells. OMIM mapping confirmed by DO. [SN]. |
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ID |
http://purl.obolibrary.org/obo/DOID_2571 |
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comment |
OMIM mapping confirmed by DO. [SN]. |
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database_cross_reference |
ICD10CM:C96.0 ICD10CM:C96.6 OMIM:604856 SNOMEDCT_US_2021_09_01:234439008 MESH:D006646 MESH:C538636 NCI:C3107 UMLS_CUI:C0019621 SNOMEDCT_US_2021_09_01:154583006 OMIM:246400 ICD9CM:202.5 NCI:C3160 UMLS_CUI:C0023381 |
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definition |
A histiocytosis that is characterized by clonal proliferation of Langerhans cells. OMIM mapping confirmed by DO. [SN]. |
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has_alternative_id |
DOID:10624 DOID:10620 DOID:2554 DOID:10623 DOID:2553 DOID:10625 DOID:10617 DOID:9582 DOID:10618 |
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has_exact_synonym |
Histiocytosis X Letterer-Siwe disease of lymph nodes of multiple sites Letterer-Siwe disease involving intrathoracic lymph nodes Letterer-Siwe disease of lymph nodes of inguinal region and lower limb Letterer-Siwe disease involving lymph nodes of axilla and upper limb Langerhan's cell histiocytosis Letterer-Siwe disease of spleen Letterer-Siwe disease of intrathoracic lymph nodes Letterer-Siwe disease Letterer-Siwe disease of lymph nodes of inguinal region amd/or lower limb Letterer-Siwe disease of lymph nodes of axilla and/or upper limb Letterer-Siwe disease involving lymph nodes of head, face and neck Letterer-Siwe disease involving lymph nodes of head, face, and neck Letterer-Siwe disease involving intra-abdominal lymph nodes Letterer-Siwe disease involving lymph nodes of multiple sites Langerhans cell granulomatosis Letterer-Siwe disease of lymph nodes of head, face and neck Letterer-Siwe disease of lymph nodes of head, face and/or neck Letterer-Siwe disease involving intrapelvic lymph nodes Letterer-Siwe disease of lymph nodes of axilla and upper limb Letterer-Siwe disease of intra-abdominal lymph nodes Letterer-Siwe disease of lymph nodes of inguinal region and/or lower limb Letterer-Siwe disease involving lymph nodes of inguinal region and lower limb Letterer-Siwe disease of intrapelvic lymph nodes Letterer-Siwe disease involving spleen |
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has_obo_namespace |
disease_ontology |
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IAO_0000115 |
A histiocytosis that is characterized by clonal proliferation of Langerhans cells. |
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id |
DOID:2571 |
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in_subset | ||
label |
Langerhans-cell histiocytosis |
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notation |
DOID:2571 |
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note |
A histiocytosis that is characterized by clonal proliferation of Langerhans cells. OMIM mapping confirmed by DO. [SN]. |
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prefLabel |
Langerhans-cell histiocytosis |
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subClassOf |