loading...| Preferred Name |
Dermatofibrosarcoma |
|
| Synonyms |
Giant Cell Fibroblastomas |
|
| Definitions |
A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA. |
|
| ID |
http://purl.bioontology.org/ontology/MESH/D018223 |
|
| altLabel |
Giant Cell Fibroblastomas Tumor, Darier-Ferrand Fibrosarcomatous Dermatofibrosarcoma Protuberans Bednars Tumor Pigmented DFSPs Dermatofibrosarcoma Protuberan, Myxoid Dermatofibrosarcoma Protuberans, Myxoid Metastatic Dermatofibrosarcoma Protuberan Dermatofibrosarcoma Protuberans, Familial Myxoid DFSP Dermatofibrosarcoma Protuberan, Metastatic Myxoid DFSPs DFSP, Juvenile Dermatofibrosarcoma Protuberan, Fibrosarcomatous DFSPs, Juvenile Darier-Hoffmann Tumor Dermatofibrosarcoma Protuberan, Familial Protuberans, Dermatofibrosarcoma DFSP, Pigmented Fibroblastomas, Giant Cell Bednar Tumor Protuberan, Giant Dermatofibrosarcoma DFSPs, Pigmented DFSP, Myxoid Protuberan, Myxoid Dermatofibrosarcoma DFSP, Fibrosarcomatous Fibrosarcomatous Dermatofibrosarcoma Protuberan Dermatofibrosarcoma Protuberan, Giant Metastatic Dermatofibrosarcoma Protuberans FS-DFSP Dermatofibrosarcoma Protuberan, Pigmented Pigmented Dermatofibrosarcoma Protuberan Protuberans, Metastatic Dermatofibrosarcoma DFSPs, Fibrosarcomatous Myxoid Dermatofibrosarcoma Protuberans Dermatofibrosarcoma Protuberan Cell Fibroblastoma, Giant Protuberan, Fibrosarcomatous Dermatofibrosarcoma Protuberans, Pigmented Dermatofibrosarcoma Dermatofibrosarcoma Protuberans Giant Dermatofibrosarcoma Protuberans Familial Dermatofibrosarcoma Protuberans Darier Hoffmann Tumor Tumor, Bednar Protuberan, Familial Dermatofibrosarcoma Dermatofibrosarcoma Protuberans, Giant Protuberans, Giant Dermatofibrosarcoma Dermatofibrosarcoma Protuberans, Giant Cell Protuberan, Dermatofibrosarcoma Cell Fibroblastomas, Giant Juvenile DFSP Giant Cell Fibroblastoma DFSPs, Myxoid Protuberans, Familial Dermatofibrosarcoma Dermatofibrosarcoma Protuberans, Fibrosarcomatous Fibroblastoma, Giant Cell Bednar's Tumor Dermatofibrosarcoma Protuberans, Metastatic Protuberan, Metastatic Dermatofibrosarcoma Giant Dermatofibrosarcoma Protuberan Darier-Ferrand Tumor Protuberans, Myxoid Dermatofibrosarcoma Fibrosarcomatous DFSP Protuberans, Fibrosarcomatous Dermatofibrosarcoma Juvenile DFSPs Pigmented Dermatofibrosarcoma Protuberans Darier Ferrand Tumor Dermatofibrosarcoma Protuberans, Pigmented Myxoid Dermatofibrosarcoma Protuberan Dermatofibrosarcomas Fibrosarcomatous DFSPs Familial Dermatofibrosarcoma Protuberan Pigmented DFSP Protuberan, Pigmented Dermatofibrosarcoma Tumor, Darier-Hoffmann Tumor, Bednar's |
|
| AN |
coordinate with with SKIN NEOPLASMS |
|
| AQL |
BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI |
|
| cui |
C3693482 C3665732 C0206647 C0334464 C0334454 |
|
| DC |
1 |
|
| definition |
A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA. |
|
| DX |
19940101 |
|
| HN |
94 |
|
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000098 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000556 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
| Machine permutation |
94 |
|
| MDA |
19930625 |
|
| MMR |
20140613 |
|
| MN |
C04.557.450.565.590.350.320 C04.557.450.795.350.320 |
|
| notation |
D018223 |
|
| prefLabel |
Dermatofibrosarcoma |
|
| TERMUI |
T853291 T853292 T853272 T853276 T841260 T853273 T853289 T853279 T841261 T853288 T853294 T853278 T853275 T853170 T054495 T853290 T853280 T853293 T853274 T853277 T853281 |
|
| TH |
OMIM (2013) NLM (2015) NLM (1994) GHR (2014) ORD (2010) |
|
| tui |
T191 |
|
| subClassOf |