Preferred Name |
Granulomatosis with Polyangiitis |
|
Synonyms |
Wegener's Granulomatosis |
|
Definitions |
A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN. |
|
ID |
http://purl.bioontology.org/ontology/MESH/D014890 |
|
altLabel |
Wegener's Granulomatosis Granulomatosis, Wegener Polyangiitis, Granulomatosis with with Polyangiitis, Granulomatosis Wegener Granulomatosis Polyangiitides, Granulomatosis with with Polyangiitides, Granulomatosis Granulomatosis with Polyangiitides Granulomatosis, Wegener's |
|
AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
|
cui |
C3495801 |
|
DC |
1 |
|
definition |
A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN. |
|
DX |
19660101 |
|
FX |
D020293 D053146 |
|
HN |
2015(1963) |
|
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
Inverse of RO | ||
Machine permutation |
2015; see Wegener Granulomatosis 2007-20014 |
|
Mapped from | ||
MDA |
19990101 |
|
MMR |
20211018 |
|
MN |
C08.381.483.950 C14.907.940.897.249.750 C17.800.862.105.875 C20.111.193.875 |
|
notation |
D014890 |
|
prefLabel |
Granulomatosis with Polyangiitis |
|
TERMUI |
T043464 T043463 T658532 T849075 |
|
TH |
OMIM (2013) NLM (1993) NLM (2015) NLM (1963) NLM (2007) ORD (2010) |
|
tui |
T047 |
|
subClassOf |