Preferred Name |
Denys-Drash syndrome |
|
Synonyms |
Syndrome de Drash Tumor de Wilms e pseudo-hermafroditismo Wilms Tumor mit Pseudohermaphroditismus Drash-Syndrom Síndrome de Drash Drash syndrome |
|
ID |
http://www.limics.org/hrdo/rdfns#pat_id_3552 |
|
ageOfOnset |
Neonatal/infancy Neonatale/prima infanzia Neonatal/infância Neonatal/infancy Neonatal / infancia Néonatal/petite enfance Neonatal/Kleinkindalter |
|
altLabel |
Syndrome de Drash Tumor de Wilms e pseudo-hermafroditismo Wilms Tumor mit Pseudohermaphroditismus Drash-Syndrom Síndrome de Drash Drash syndrome Tumeur de Wilms - pseudohermaphrodisme Tumore di Wilms - pseudoermafroditismo Wilms tumor and pseudohermaphroditism Sindrome di Drash Drash, síndrome de |
|
id_MedDRA |
10070179 |
|
id_Medline | ||
id_MeSH |
D030321 |
|
id_MIM |
194080 |
|
id_OMS |
N04.1 |
|
id_Orpha |
220 |
|
id_SNOMEDCT |
236385009 |
|
id_UMLS |
C0950121 |
|
patType |
disease |
|
prefixIRI |
hrdo:pat_id_3552 |
|
prefLabel |
Síndrome de Denys-Drash Denys-Drash syndrome Denys-Drash-Syndrom Síndrome de Denys-Drash Sindrome di Denys-Drash Syndrome de Denys-Drash |
|
prevalence |
<1 / 1 000 000 <1 / 1 000 000 <1 / 1 000 000 <1 / 1 000 000 <1 / 1 000 000 <1 / 1 000 000 <1 / 1 000 000 |
|
subClassOf |