Preferred Name |
CREST syndrome |
|
Synonyms |
Calcinosis - Raynaud phenomenon - esophageal involvement - sclerodactyly - telangiectasia |
|
ID |
http://www.limics.org/hrdo/rdfns#pat_id_12001 |
|
ageOfDeath |
Adult Adulto Adult Erwachsene Adulti Adultos Adulte |
|
ageOfOnset |
Erwachsenenalter Adulte La edad adulta Età adulta Adulthood Adulthood Idade adulta |
|
altLabel |
Calcinosis - Raynaud phenomenon - esophageal involvement - sclerodactyly - telangiectasia Calzinosis - Raynaud Phänomen - ösophageale Dysfunktion - Sklerodaktylie - Telangiektasie Calcinosis - fenómeno de Raynaud - afectación esofágica - esclerodactilia - telangiectasia Calcinose - maladie de Raynaud - troubles moteurs oesophagiens - sclérodactylie - télangiectasie |
|
id_MedDRA |
10011380 |
|
id_Medline |
neant |
|
id_MeSH |
D017675 |
|
id_MIM |
181750 |
|
id_OMS |
M34.1 |
|
id_Orpha |
90290 |
|
id_SNOMEDCT |
31848007 |
|
id_UMLS |
C0206138 |
|
inheritance |
Esporádico Sporadic Sporadisch Sporadique Sporadica Sporadic Esporádica |
|
patType |
disease |
|
prefixIRI |
hrdo:pat_id_12001 |
|
prefLabel |
Síndrome CREST (calcinose - fenómeno de Raynaud - envolvimento esofágico - esclerodactilia - telangiectasia Sindrome CREST CREST-Syndrom Síndrome CREST CREST syndrome Syndrome CREST |
|
prevalence |
1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 |
|
subClassOf |