Preferred Name

Desmoplastic small round cell tumor

Synonyms

DSRCT

ID

http://www.limics.org/hrdo/rdfns#pat_id_11579

ageOfOnset

Adolescent / adulte jeune

Jugendalter / junges Erwachsenenalter

Adolescencia / Edad adulta

Adolescence / Young adulthood

Adolescence / Young adulthood

Adolescenza / Giovane età adulta

Adolescência / Adulto jovem

altLabel

DSRCT

DSRCT

DSRCT

DSRCT

DSRCT

Tumeur desmoplastique à petites cellules rondes

id_MedDRA

10064581

id_Medline

http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=DetailsSearch&Term=Desmoplastic+small+round+cell%5Bti%5D+OR+(Desmoplastic+small+round+cell%5Btw%5D+Carcinoma,+Small+Cell)

id_MeSH

D058405

id_OMS

C48.2

id_Orpha

83469

id_SNOMEDCT

128735004

id_UMLS

C0281508

inheritance

Esporádico

Sporadic

Sporadisch

Sporadique

Sporadica

Sporadic

Esporádica

patType

disease

prefixIRI

hrdo:pat_id_11579

prefLabel

Tumor desmoplásico de células pequeñas y redondas

Tumeur desmoplastique à petites cellules

Desmoplastic small round cell tumor

Tumor de células pequenas redondas desmoplásicas

Rundzelltumor, desmoplastischer

Tumore desmoplastico a piccole cellule rotonde

prevalence

<1 / 1 000 000

<1 / 1 000 000

<1 / 1 000 000

<1 / 1 000 000

<1 / 1 000 000

<1 / 1 000 000

<1 / 1 000 000

subClassOf

http://www.limics.org/hrdo/rdfns#typ_id_11

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