loading...| Preferred Name |
Arrhythmogenic right ventricular dysplasia |
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| Synonyms |
Arrhythmogenic right ventricular cardiomyopathy ARVC ARVD |
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| Definitions |
Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias. and progressive right ventricular or biventricular failure. ARCVD is a major cause of sudden death in the young and among athletes. |
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| ID |
http://www.orpha.net/ORDO/Orphanet_247 |
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| database_cross_reference |
ICD10:I42.8 OMIM:600996 OMIM:609040 UMLS:C0349788 OMIM:610193 MedDRA:10058093 OMIM:607450 MeSH:D019571 OMIM:604400 OMIM:610476 OMIM:615616 OMIM:611528 |
|
| definition |
Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias. and progressive right ventricular or biventricular failure. ARCVD is a major cause of sudden death in the young and among athletes. |
|
| definition_citation |
orphanet |
|
| has_exact_synonym |
Arrhythmogenic right ventricular cardiomyopathy ARVC ARVD |
|
| label |
Arrhythmogenic right ventricular dysplasia |
|
| preferred label |
Arrhythmogenic right ventricular dysplasia |
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| prefLabel |
Arrhythmogenic right ventricular dysplasia |
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| subClassOf |