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Digital medicine Outcomes Value Set (DOVeS) Ontology
Last uploaded:
December 13, 2023
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| Preferred Name | diffuse cutaneous mastocytosis | |
| Synonyms |
DCM diffuse cutaneous mastocytosis diffuse cutaneous maculopapulous mastocytosis |
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| Definitions |
Diffuse cutaneous mastocytosis (DCM) is a rare form of cutaneous mastocytosis (CM) characterized by generalized erythroderma, various degrees of blistering, skin with a ''peau d'orange'' appearance and the accumulation of mast cells in the skin. At least two DCM variants are recognized, one with extreme blistering (Bullous DCM) and one with infiltrations (Pseudoxanthomatous DCM). |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0019315 |
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| altLabel |
DCM diffuse cutaneous mastocytosis diffuse cutaneous maculopapulous mastocytosis
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| definition |
Diffuse cutaneous mastocytosis (DCM) is a rare form of cutaneous mastocytosis (CM) characterized by generalized erythroderma, various degrees of blistering, skin with a ''peau d'orange'' appearance and the accumulation of mast cells in the skin. At least two DCM variants are recognized, one with extreme blistering (Bullous DCM) and one with infiltrations (Pseudoxanthomatous DCM).
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| has_broad_synonym |
DCM
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| has_exact_synonym |
diffuse cutaneous mastocytosis diffuse cutaneous maculopapulous mastocytosis
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| label |
diffuse cutaneous mastocytosis
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| prefixIRI |
MONDO:0019315
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| prefLabel |
diffuse cutaneous mastocytosis
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| textual definition |
Diffuse cutaneous mastocytosis (DCM) is a rare form of cutaneous mastocytosis (CM) characterized by generalized erythroderma, various degrees of blistering, skin with a ''peau d'orange'' appearance and the accumulation of mast cells in the skin. At least two DCM variants are recognized, one with extreme blistering (Bullous DCM) and one with infiltrations (Pseudoxanthomatous DCM).
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