Preferred Name

papillary renal cell carcinoma
Synonyms

papillary renal cell carcinoma, familial - (subtype)

papillary renal carcinoma, malignant - (subtype)

RCCP1

RCCP

renal adenocarcinoma

papillary renal cell carcinoma, sporadic - (subtype)

renal cell carcinoma, papillary, 1

chromophil RCC

papillary renal cell carcinoma, multiple - (subtype)

papillary renal cell carcinoma, bilateral - (subtype)

papillary renal cell adenocarcinoma

HPRCC

papillary renal cell cancer

papillary (chromophil) renal cell carcinoma

renal cell carcinoma, papillary, type 1

papillary kidney carcinoma

chromophil carcinoma of kidney

chromophil renal cell carcinoma

sporadic papillary renal cell carcinoma

chromophil carcinoma of the kidney

papillary renal cell carcinoma

Definitions

A rare subtype of renal cell carcinoma, arising from the renal tubular epithelium and showing a papillary growth pattern, which typically manifests with hematuria, flank pain, palpable abdominal mass or nonspecific symptoms, such as fatigue, weight loss or fever. Symptoms related to metastatic spread, such as bone pain or persistent cough, are frequently associated since early diagnosis is not common. It is typically multifocal, bilateral, and in most cases sporadic, although different hereditary syndromes, such as Hereditary leiomyoma renal cell carcinoma, Birt-Hogg-DubC) syndrome and Tuberous sclerosis, may predispose to the development of papillary renal cell carcinoma.

ID

http://purl.obolibrary.org/obo/MONDO_0017884

altLabel

papillary renal cell carcinoma, familial - (subtype)

papillary renal carcinoma, malignant - (subtype)

RCCP1

RCCP

renal adenocarcinoma

papillary renal cell carcinoma, sporadic - (subtype)

renal cell carcinoma, papillary, 1

chromophil RCC

papillary renal cell carcinoma, multiple - (subtype)

papillary renal cell carcinoma, bilateral - (subtype)

papillary renal cell adenocarcinoma

HPRCC

papillary renal cell cancer

papillary (chromophil) renal cell carcinoma

renal cell carcinoma, papillary, type 1

papillary kidney carcinoma

chromophil carcinoma of kidney

chromophil renal cell carcinoma

sporadic papillary renal cell carcinoma

chromophil carcinoma of the kidney

papillary renal cell carcinoma

definition

A rare subtype of renal cell carcinoma, arising from the renal tubular epithelium and showing a papillary growth pattern, which typically manifests with hematuria, flank pain, palpable abdominal mass or nonspecific symptoms, such as fatigue, weight loss or fever. Symptoms related to metastatic spread, such as bone pain or persistent cough, are frequently associated since early diagnosis is not common. It is typically multifocal, bilateral, and in most cases sporadic, although different hereditary syndromes, such as Hereditary leiomyoma renal cell carcinoma, Birt-Hogg-DubC) syndrome and Tuberous sclerosis, may predispose to the development of papillary renal cell carcinoma.

has_exact_synonym

papillary renal cell adenocarcinoma

HPRCC

papillary renal cell cancer

papillary (chromophil) renal cell carcinoma

renal cell carcinoma, papillary, type 1

papillary kidney carcinoma

chromophil carcinoma of kidney

chromophil renal cell carcinoma

sporadic papillary renal cell carcinoma

chromophil carcinoma of the kidney

papillary renal cell carcinoma

has_related_synonym

papillary renal cell carcinoma, familial - (subtype)

papillary renal carcinoma, malignant - (subtype)

RCCP1

RCCP

renal adenocarcinoma

papillary renal cell carcinoma, sporadic - (subtype)

renal cell carcinoma, papillary, 1

chromophil RCC

papillary renal cell carcinoma, multiple - (subtype)

papillary renal cell carcinoma, bilateral - (subtype)

label

papillary renal cell carcinoma

prefixIRI

MONDO:0017884

prefLabel

papillary renal cell carcinoma

seeAlso

https://rarediseases.info.nih.gov/diseases/9572/papillary-renal-cell-carcinoma

textual definition

A rare subtype of renal cell carcinoma, arising from the renal tubular epithelium and showing a papillary growth pattern, which typically manifests with hematuria, flank pain, palpable abdominal mass or nonspecific symptoms, such as fatigue, weight loss or fever. Symptoms related to metastatic spread, such as bone pain or persistent cough, are frequently associated since early diagnosis is not common. It is typically multifocal, bilateral, and in most cases sporadic, although different hereditary syndromes, such as Hereditary leiomyoma renal cell carcinoma, Birt-Hogg-DubC) syndrome and Tuberous sclerosis, may predispose to the development of papillary renal cell carcinoma.

subClassOf

http://purl.obolibrary.org/obo/MONDO_0005549

http://purl.obolibrary.org/obo/MONDO_0002512

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