loading...| Preferred Name | epithelioid sarcoma | |
| Synonyms |
ES epithelioid sarcoma epithelioid cell sarcoma |
|
| Definitions |
An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma). |
|
| ID |
http://purl.obolibrary.org/obo/MONDO_0017387 |
|
| altLabel |
ES epithelioid sarcoma epithelioid cell sarcoma |
|
| definition |
An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma). |
|
| has_exact_synonym |
ES epithelioid sarcoma epithelioid cell sarcoma |
|
| label |
epithelioid sarcoma |
|
| prefixIRI |
MONDO:0017387 |
|
| prefLabel |
epithelioid sarcoma |
|
| seeAlso |
https://rarediseases.info.nih.gov/diseases/10181/epithelioid-sarcoma |
|
| textual definition |
An aggressive malignant neoplasm of uncertain differentiation, characterized by the presence of epithelioid cells forming nodular patterns. The nodules often undergo central necrosis, resulting in a pseudogranulomatous growth pattern. It usually occurs in young adults. The most common sites of involvement are the extremities (distal-type epithelioid sarcoma), and less frequently the pelvis, perineum, and genital organs (proximal-type epithelioid sarcoma). |
|
| subClassOf |