Preferred Name |
scimitar syndrome |
|
Synonyms |
hypogenetic lung syndrome congenital pulmonary venolobar syndrome Halasz syndrome Epibronchial right pulmonary vein syndrome |
|
Definitions |
Scimitar syndrome is characterized by a combination of cardiopulmonary anomalies including partial anomalous pulmonary venous return connection of the right lung to the inferior caval vein leading to the creation of a left-to-right shunt. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0015987 |
|
has_exact_synonym |
hypogenetic lung syndrome congenital pulmonary venolobar syndrome Halasz syndrome Epibronchial right pulmonary vein syndrome |
|
label |
scimitar syndrome |
|
prefixIRI |
MONDO:0015987 |
|
prefLabel |
scimitar syndrome |
|
textual definition |
Scimitar syndrome is characterized by a combination of cardiopulmonary anomalies including partial anomalous pulmonary venous return connection of the right lung to the inferior caval vein leading to the creation of a left-to-right shunt. |
|
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0020292 |