loading...| Preferred Name | primary sclerosing cholangitis | |
| Synonyms |
cholangitis, primary sclerosing PSC |
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| Definitions |
Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure. |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0013433 |
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| altLabel |
cholangitis, primary sclerosing PSC |
|
| definition |
Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure. |
|
| has_exact_synonym |
PSC |
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| has_related_synonym |
cholangitis, primary sclerosing |
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| label |
primary sclerosing cholangitis |
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| prefixIRI |
MONDO:0013433 |
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| prefLabel |
primary sclerosing cholangitis |
|
| textual definition |
Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure. |
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| subClassOf |