Preferred Name

juvenile dermatomyositis

Synonyms

juvenile dermatomyositis

childhood dermatomyositis

inflammation of myoseptum

juvenile DM

myoseptumitis

myoseptum inflammation

childhood type dermatomyositis

JPM

JDM

juvenile myositis

myositis

myopathy, familial idiopathic inflammatory

Definitions

Juvenile dermatomyositis (JDM) is the early-onset form of dermatomyositis (DM), a systemic, autoimmune inflammatory muscle disorder, characterized by proximal muscle weakness, evocative skin lesion, and systemic manifestations.

ID

http://purl.obolibrary.org/obo/MONDO_0008054

has_exact_synonym

juvenile dermatomyositis

childhood dermatomyositis

inflammation of myoseptum

juvenile DM

myoseptumitis

myoseptum inflammation

has_related_synonym

childhood type dermatomyositis

JPM

JDM

juvenile myositis

myositis

myopathy, familial idiopathic inflammatory

label

juvenile dermatomyositis

prefixIRI

MONDO:0008054

prefLabel

juvenile dermatomyositis

seeAlso

https://rarediseases.info.nih.gov/diseases/6805/juvenile-dermatomyositis

textual definition

Juvenile dermatomyositis (JDM) is the early-onset form of dermatomyositis (DM), a systemic, autoimmune inflammatory muscle disorder, characterized by proximal muscle weakness, evocative skin lesion, and systemic manifestations.

subClassOf

http://purl.obolibrary.org/obo/MONDO_0016367

http://purl.obolibrary.org/obo/MONDO_0018010

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