Preferred Name | Langerhans Cell Histiocytosis | |
Synonyms |
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ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Langerhans_Cell_Histiocytosis |
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DEFINITION |
A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognized: eosinophilic granuloma, Letterer-Siwe disease, and Hand-Schuller-Christian disease. The clinical course is generally related to the number of organs affected at presentation. (WHO, 2001) |
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FULL_SYN |
Histiocytosis X LCH Langerhans Cell Granulomatosis |
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label |
Langerhans Cell Histiocytosis |
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prefixIRI |
Thesaurus:Langerhans_Cell_Histiocytosis |
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prefLabel |
Langerhans Cell Histiocytosis |
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subClassOf |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Histiocytic_and_Dendritic_Cell_Neoplasms |
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