loading...| Preferred Name |
Desmoplastic Small Round Cell Tumor |
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| Synonyms |
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| ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Desmoplastic_Small_Round_Cell_Tumor |
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| DEFINITION |
An aggressive malignant neoplasm of uncertain lineage. It is characterized by the presence of small round cells in a desmoplastic stroma. It usually affects children and young adults. The most common site of involvement is the abdomen. Patients usually present with abdominal distention, pain, ascites, and a palpable abdominal mass. The prognosis is usually poor. |
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| FULL_SYN |
Desmoplastic Small Round-Cell Neoplasm DSRCT Desmoplastic Small Round-Cell Tumor |
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| isDefinedBy |
An aggressive malignant neoplasm of uncertain lineage. It is characterized by the presence of small round cells in a desmoplastic stroma. It usually affects children and young adults. The most common site of involvement is the abdomen. Patients usually present with abdominal distention, pain, ascites, and a palpable abdominal mass. The prognosis is usually poor. |
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| label |
Desmoplastic Small Round Cell Tumor |
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| prefixIRI |
Thesaurus:Desmoplastic_Small_Round_Cell_Tumor |
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| prefLabel |
Desmoplastic Small Round Cell Tumor |
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| Synonym |
Desmoplastic Small Round-Cell Neoplasm DSRCT Desmoplastic Small Round-Cell Tumor |
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| subClassOf |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Malignant_Miscellaneous_Mesenchymal_Neoplasm http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Soft_Tissue_Sarcoma http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Small_Cell_Sarcoma |