loading...| Preferred Name | frontotemporal dementia | |
| Synonyms |
frontotemporal lobe dementia (FLDEM) MSTD frontotemporal lobar degeneration multiple system tauopathy with presenile dementia Wilhemsen-Lynch disease pallidopontonigral degeneration FTD |
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| Definitions |
Frontotemporal dementia (FTD) comprises a group of neurodegenerative disorders, characterized by progressive changes in behavior, executive dysfunction and language impairment, as a result of degeneration of the medial prefrontal and frontoinsular cortices. Four clinical subtypes have been identified: semantic dementia, progressive non-fluent aphasia, behavioral variant FTD and right temporal lobar atrophy. |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0017276 |
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| database_cross_reference |
NANDO:1200548 MESH:D057180 MEDGEN:83266 Orphanet:282 NCIT:C84719 UMLS:C0338451 icd11.foundation:831337417 MedDRA:10068968 DOID:9255 GARD:8436 |
|
| definition |
Frontotemporal dementia (FTD) comprises a group of neurodegenerative disorders, characterized by progressive changes in behavior, executive dysfunction and language impairment, as a result of degeneration of the medial prefrontal and frontoinsular cortices. Four clinical subtypes have been identified: semantic dementia, progressive non-fluent aphasia, behavioral variant FTD and right temporal lobar atrophy. |
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| has_exact_synonym |
frontotemporal lobar degeneration multiple system tauopathy with presenile dementia Wilhemsen-Lynch disease pallidopontonigral degeneration FTD |
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| has_related_synonym |
frontotemporal lobe dementia (FLDEM) MSTD |
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| id |
MONDO:0017276 |
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| in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_group_of_disorders http://purl.obolibrary.org/obo/mondo/mondo-base#disease_grouping |
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| label |
frontotemporal dementia |
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| notation |
MONDO:0017276 |
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| preferred label |
frontotemporal dementia |
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| prefLabel |
frontotemporal dementia |
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| skos_closeMatch | ||
| skos_exactMatch |
http://linkedlifedata.com/resource/umls/id/C0338451 http://purl.obolibrary.org/obo/Orphanet_282 http://identifiers.org/mesh/D057180 http://identifiers.org/medgen/83266 http://purl.obolibrary.org/obo/NCIT_C84719 http://purl.obolibrary.org/obo/mondo/sources/icd11foundation/831337417 |
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| subClassOf | ||
| excluded_subClassOf |