Preferred Name | pleomorphic xanthoastrocytoma | |
Synonyms |
pleomorphic Xantho-astrocytoma PXA |
|
Definitions |
A WHO grade ll astrocytic tumor with a relatively favorable prognosis. It is characterized by pleomorphic and lipidized cells expressing GFAP often surrounded by a reticulin network and eosinophilic granular bodies. It presents in the superficial cerebral hemispheres and involves the meninges. It typically affects children and young adults. |
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ID |
http://purl.obolibrary.org/obo/MONDO_0016690 |
|
database_cross_reference |
ICDO:9424/3 ONCOTREE:PXA MEDGEN:137786 Orphanet:251607 UMLS:C0334586 DOID:4852 GARD:10631 NCIT:C4323 |
|
definition |
A WHO grade ll astrocytic tumor with a relatively favorable prognosis. It is characterized by pleomorphic and lipidized cells expressing GFAP often surrounded by a reticulin network and eosinophilic granular bodies. It presents in the superficial cerebral hemispheres and involves the meninges. It typically affects children and young adults. |
|
has_exact_synonym |
pleomorphic Xantho-astrocytoma PXA |
|
id |
MONDO:0016690 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#orphanet_rare http://purl.obolibrary.org/obo/mondo/mondo-base#nord_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_disorder |
|
label |
pleomorphic xanthoastrocytoma |
|
notation |
MONDO:0016690 |
|
preferred label |
pleomorphic xanthoastrocytoma |
|
prefLabel |
pleomorphic xanthoastrocytoma |
|
see also |
https://rarediseases.info.nih.gov/diseases/10631/pleomorphic-xanthoastrocytoma |
|
skos_exactMatch |
http://purl.obolibrary.org/obo/Orphanet_251607 http://linkedlifedata.com/resource/umls/id/C0334586 http://identifiers.org/medgen/137786 |
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subClassOf |