Preferred Name | Neurofibroma | |
Synonyms |
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|
ID |
http://bioontology.org/projects/ontologies/birnlex#birnlex_12604 |
|
abbrev | ||
class_or_indiv |
true |
|
definition |
A moderately firm, benign, encapsulated tumor resulting from proliferation of SCHWANN CELLS and FIBROBLASTS that includes portions of nerve fibers. The tumors usually develop along peripheral or cranial nerves and are a central feature of NEUROFIBROMATOSIS 1, where they may occur intracranially or involve spinal roots. Pathologic features include fusiform enlargement of the involved nerve. Microscopic examination reveals a disorganized and loose cellular pattern with elongated nuclei intermixed with fibrous strands (MeSH). |
|
external_id_urls |
http://www.nlm.nih.gov/cgi/mesh/2008/MB_cgi?field=uid&term=D009455 |
|
external_ids |
meshUID:D009455 |
|
label |
Neurofibroma |
|
mod_date |
2007-10-05 |
|
preferred_label |
Neurofibroma |
|
prefixIRI |
birnlex_12604 |
|
prefLabel |
Neurofibroma |
|
retired |
false |
|
synonyms | ||
subClassOf |
http://bioontology.org/projects/ontologies/birnlex#birnlex_12602 |