loading...| Preferred Name |
Congenital hepatic fibrosis |
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| Synonyms |
Excessive buildup of connective tissue and scarring of liver at birth Congenital liver fibrosis |
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| Definitions |
Congenital hepatic fibrosis is characterized by enlarged portal tracts with extensive fibrosis and numerous bile ductules that communicate with the bile tree. The affected area tends to be sharply demarcated from normal liver parenchyma and does not display regenerative nodules (which distinguished the condition from cirrhosis). The presence of fibrosis of that part of the liver with congenital onset. |
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| ID |
http://purl.obolibrary.org/obo/HP_0002612 |
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| comment |
Congenital hepatic fibrosis is characterized by enlarged portal tracts with extensive fibrosis and numerous bile ductules that communicate with the bile tree. The affected area tends to be sharply demarcated from normal liver parenchyma and does not display regenerative nodules (which distinguished the condition from cirrhosis). |
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| database_cross_reference |
SNOMEDCT_US:79607001 MSH:C562378 UMLS:C0009714 |
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| definition |
The presence of fibrosis of that part of the liver with congenital onset. |
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| has exact synonym |
Excessive buildup of connective tissue and scarring of liver at birth Congenital liver fibrosis |
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| id |
HP:0002612 |
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| label |
Congenital hepatic fibrosis |
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| notation |
HP:0002612 |
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| prefLabel |
Congenital hepatic fibrosis |
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| subClassOf |