loading...| Preferred Name |
Inflammatory myofibroblastic tumor |
|
| Synonyms |
Inflammatory myofibroblastic tumour Inflammatory myofibroblastic tumor (disorder) |
|
| Definitions |
A rare neoplastic lesion of the submucosal stroma, which can develop in any organ, often occurring in the lung, mesentery, omentum and the retroperitoneal region. It is histologically heterogenous, composed of spindle-shaped cells, myofibroblasts and inflammatory cells. It is usually benign, however local invasion, recurrence, malignant transformation with vascular invasion and metastases may occur. The presentation is nonspecific and depends on the organ involved. Some patients may present with paraneoplastic syndrome (fever, malaise, weight loss, thrombocytosis) or symptoms related to compression of adjacent organs, such as bowel obstruction. |
|
| ID |
http://purl.bioontology.org/ontology/SNOMEDCT/771233008 |
|
| Active |
1 |
|
| altLabel |
Inflammatory myofibroblastic tumour Inflammatory myofibroblastic tumor (disorder) |
|
| CASE SIGNIFICANCE ID |
900000000000448009 |
|
| CTV3ID |
XV6xf |
|
| cui |
C0334121 |
|
| definition |
A rare neoplastic lesion of the submucosal stroma, which can develop in any organ, often occurring in the lung, mesentery, omentum and the retroperitoneal region. It is histologically heterogenous, composed of spindle-shaped cells, myofibroblasts and inflammatory cells. It is usually benign, however local invasion, recurrence, malignant transformation with vascular invasion and metastases may occur. The presentation is nonspecific and depends on the organ involved. Some patients may present with paraneoplastic syndrome (fever, malaise, weight loss, thrombocytosis) or symptoms related to compression of adjacent organs, such as bowel obstruction. |
|
| DEFINITION STATUS ID |
900000000000073002 |
|
| Effective time |
20190131 |
|
| Has associated morphology | ||
| notation |
771233008 |
|
| prefLabel |
Inflammatory myofibroblastic tumor |
|
| Subset member |
900000000000497000~MAPTARGET~XV6xf 447562003~MAPRULE~TRUE 6011000124106~MAPGROUP~1 447562003~MAPGROUP~1 447562003~CORRELATIONID~447561005 447562003~MAPTARGET~D48.9 6011000124106~MAPCATEGORYID~447637006 447562003~MAPADVICE~ALWAYS D48.9 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE 900000000000509007~ACCEPTABILITYID~900000000000548007 900000000000508004~ACCEPTABILITYID~900000000000548007 6011000124106~MAPADVICE~ALWAYS D48.9 447562003~MAPPRIORITY~1 447562003~MAPCATEGORYID~447637006 6011000124106~MAPPRIORITY~1 6011000124106~CORRELATIONID~447561005 6011000124106~MAPRULE~TRUE 6011000124106~MAPTARGET~D48.9 |
|
| tui |
T191 |
|
| Type ID |
900000000000003001 900000000000013009 |
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| subClassOf |