Physician Data Query

Last uploaded: January 31, 2024
Preferred Name

paraganglioma

Synonyms

Neoplasm of the Paraganglion

Tumor of Paraganglion

Definitions

A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. Check for "https://www.cancer.gov/about-cancer/treatment/clinical-trials/intervention/C3308" active clinical trials using this agent. ("http://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI%20Thesaurus&code=C3308" NCI Thesaurus)

ID

http://purl.bioontology.org/ontology/PDQ/CDR0000639696

altLabel

Neoplasm of the Paraganglion

Tumor of the Paraganglion

Paraganglion Neoplasm

Paraganglionic Neoplasm

Paraganglionic Tumor

Paraganglion Tumor

Neoplasm of Paraganglion

Tumor of Paraganglion

Associated genetic condition

http://purl.bioontology.org/ontology/PDQ/CDR0000042846

http://purl.bioontology.org/ontology/PDQ/CDR0000042845

http://purl.bioontology.org/ontology/PDQ/CDR0000654716

http://purl.bioontology.org/ontology/PDQ/CDR0000654673

cui

C0030421

DATE FIRST PUBLISHED

2009-03-31

Date last modified

2017-03-30

definition

A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. Check for "https://www.cancer.gov/about-cancer/treatment/clinical-trials/intervention/C3308" active clinical trials using this agent. ("http://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI%20Thesaurus&code=C3308" NCI Thesaurus)

NCI ID

C3308

notation

CDR0000639696

ORIG STY

Neoplasm diagnosis

prefLabel

paraganglioma

tui

T191

subClassOf

http://purl.bioontology.org/ontology/PDQ/CDR0000550683

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MDRGER/10061332 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10033792 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10073860 MDRGER CUI
http://purl.bioontology.org/ontology/SCTSPA/127027008 SCTSPA CUI
http://purl.bioontology.org/ontology/RCD/X77oB RCD CUI
http://purl.bioontology.org/ontology/OMIM/MTHU004448 OMIM CUI
http://purl.bioontology.org/ontology/SCTSPA/803009 SCTSPA CUI
http://purl.bioontology.org/ontology/RCD/Xa99M RCD CUI
http://purl.bioontology.org/ontology/MDRFRE/10033792 MDRFRE CUI
http://purl.bioontology.org/ontology/SCTSPA/72787006 SCTSPA CUI
http://purl.bioontology.org/ontology/SNOMEDCT/72787006 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SNMI/M-86830 SNMI CUI
http://purl.bioontology.org/ontology/MEDDRA/10073860 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRFRE/10073860 MDRFRE CUI
http://purl.bioontology.org/ontology/SCTSPA/253029009 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/MTHU015031 OMIM CUI
http://purl.bioontology.org/ontology/MDRFRE/10061332 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10061332 MEDDRA CUI
http://purl.bioontology.org/ontology/MSHFRE/D010235 MSHFRE CUI
http://purl.bioontology.org/ontology/MESH/D010235 MESH CUI
http://purl.bioontology.org/ontology/NDFRT/N0000002299 NDFRT CUI
http://purl.bioontology.org/ontology/SNOMEDCT/127027008 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MEDDRA/10033792 MEDDRA CUI
http://purl.bioontology.org/ontology/SNMI/M-86801 SNMI CUI
http://purl.bioontology.org/ontology/SCTSPA/302833002 SCTSPA CUI
http://purl.bioontology.org/ontology/SNOMEDCT/302833002 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SNOMEDCT/253029009 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SNOMEDCT/803009 SNOMEDCT CUI
http://www.ebi.ac.uk/efo/EFO_1000453 EFO LOOM
http://purl.obolibrary.org/obo/DOID_0050773 DOID LOOM
http://purl.obolibrary.org/obo/MONDO_0000448 MONDO LOOM
http://purl.obolibrary.org/obo/MONDO_0000448 OBA LOOM
http://purl.obolibrary.org/obo/MPATH_403 MPATH LOOM
http://www.gamuts.net/entity#paraganglioma GAMUTS LOOM
http://purl.bioontology.org/ontology/RCD/Xa99M RCD LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.465.625.650.700 RH-MESH LOOM
http://purl.obolibrary.org/obo/MONDO_0000448 DOVES LOOM
http://www.semanticweb.org/ontologies/2012/11/abnormalities.owl#phenodb:2408 IFAR LOOM
http://radlex.org/RID/RID4512 RADLEX LOOM
http://doe-generated-ontology.com/OntoAD#C0030421 ONTOAD LOOM
http://purl.obolibrary.org/obo/DOID_0050773 DTO LOOM
http://purl.obolibrary.org/obo/DOID_0050773 BAO LOOM
http://purl.obolibrary.org/obo/DOID_0050773 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0050773 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0050773 FNS-H LOOM
http://purl.bioontology.org/ontology/MEDDRA/10073860 MEDDRA LOOM
http://www.phoc.org.cn/pmo/class/PMO_00085363 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU015031 OMIM LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3308 NCIT LOOM
http://purl.jp/bio/4/id/200906064578708779 IOBC LOOM
http://purl.bioontology.org/ontology/MESH/D010235 MESH LOOM
http://purl.obolibrary.org/obo/OMIT_0011232 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D010235 RH-MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#9261 OCHV LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/302833002 SNOMEDCT LOOM
http://id.nlm.nih.gov/mesh/D010235 MDM LOOM
http://purl.obolibrary.org/obo/NCIT_C3308 BERO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/803009 SNOMEDCT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Paraganglionic_Neoplasm CSEO LOOM
http://purl.obolibrary.org/obo/HP_0002668 HP LOOM
http://purl.obolibrary.org/obo/HP_0002668 UPHENO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0030421 OCHV LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.580.625.650.700 RH-MESH LOOM