Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Dedifferentiated liposarcoma

Synonyms

DDLS

Definitions

Dedifferentiated liposarcoma (DDLS) is a high-grade subtype of liposarcoma (LS; see this term) that progresses from well-differentiated liposarcoma (WDLS; see this term), and most often occurs in the retroperitoneum. It is defined as a region of nonlipogenic sarcoma associated with WDLS. .

ID

http://www.orpha.net/ORDO/Orphanet_99970

alternative_term

DDLS

definition

Dedifferentiated liposarcoma (DDLS) is a high-grade subtype of liposarcoma (LS; see this term) that progresses from well-differentiated liposarcoma (WDLS; see this term), and most often occurs in the retroperitoneum. It is defined as a region of nonlipogenic sarcoma associated with WDLS. .

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=99970

has_age_of_onset

Adult

has_inheritance

Not applicable

hasDbXref

ICD-10:C49.9

UMLS:C0205824

MedDRA:10073135

label

Dedifferentiated liposarcoma

notation

ORPHA:99970

Histopathological subtype

part_of

http://www.orpha.net/ORDO/Orphanet_69078

prefixIRI

ORDO:Orphanet_99970

prefLabel

Dedifferentiated liposarcoma

present_in

Europe AND has_annual_incidence_average_value : 0.27 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_point_prevalence_range : Unknown

treeView

http://www.orpha.net/ORDO/Orphanet_69078

subClassOf

http://www.orpha.net/ORDO/Orphanet_557494

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