Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Hodgkin lymphoma

Synonyms
Definitions

Hodgkin lymphoma (HL) is a heterogeneous group of malignant lymphoid neoplasms of B-cell origin characterized histologically by the presence of Hodgkin and Reed-Sternberg (HRS) cells in the vast majority of cases.

ID

http://www.orpha.net/ORDO/Orphanet_98293

definition

Hodgkin lymphoma (HL) is a heterogeneous group of malignant lymphoid neoplasms of B-cell origin characterized histologically by the presence of Hodgkin and Reed-Sternberg (HRS) cells in the vast majority of cases.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=98293

has_age_of_onset

Adolescent

Adult

Childhood

Elderly

Infancy

has_inheritance

Multigenic/multifactorial

hasDbXref

UMLS:C0019829

MeSH:D006689

ICD-11:2B30

label

Hodgkin lymphoma

notation

ORPHA:98293

Clinical group

prefixIRI

ORDO:Orphanet_98293

prefLabel

Hodgkin lymphoma

present_in

United States AND has_annual_incidence_average_value : 2.8 AND has_annual_incidence_range : 1-9 / 100 000

China AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000

Japan AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000

Europe AND has_annual_incidence_average_value : 2.4 AND has_annual_incidence_range : 1-9 / 100 000

Europe AND has_lifetime_prevalence_average_value : 46.9 AND has_lifetime_prevalence_range : 1-5 / 10 000

subClassOf

http://www.orpha.net/ORDO/Orphanet_557492

http://www.orpha.net/ORDO/Orphanet_223735

http://www.orpha.net/ORDO/Orphanet_289644

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Delete Mapping To Ontology Source
http://nanbyodata.jp/ontology/NANDO_2200024 NANDO LOOM
http://purl.bioontology.org/ontology/ICD10CM/C81 ICD10CM LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C9357 NCIT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Hodgkin_s_Lymphoma CSEO LOOM
http://radlex.org/RID/RID3842 RADLEX LOOM
http://www.semanticweb.org/ontologies/2012/11/abnormalities.owl#phenodb:2512 IFAR LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000041646 PDQ LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU014312 OMIM LOOM
http://www.limics.org/hrdo/rdfns#pat_id_13310 HRDO LOOM
http://purl.obolibrary.org/obo/NCIT_C9357 BERO LOOM
http://localhost/plosthes.2017-1#9888 PLOSTHES LOOM
urn:agi-pathway:uuid-037e2c70-b0f5-470b-aa15-d86985cf0301 BPT LOOM
http://purl.obolibrary.org/obo/HP_0012189 HP LOOM
http://purl.obolibrary.org/obo/HP_0012189 UPHENO LOOM
http://vocab.vodan-totafrica.info/vodana-terms/vdiseases/2B30 VODANADISEASES LOOM
http://purl.bioontology.org/ontology/LNC/LA26792-4 LOINC LOOM
http://identifiers.org/omim/236000 REXO LOOM
http://identifiers.org/omim/236000 GEXO LOOM
http://identifiers.org/omim/236000 RETO LOOM
http://www.phoc.org.cn/pmo/class/PMO_00001240 PMAPP-PMO LOOM
http://www.semanticweb.org/ontologies/STO.owl#OWLClass_6fa705db_1014_4bbe_9e37_32983237e8d4 STO-DRAFT LOOM
http://www.semanticweb.org/ontologies/STO.owl#OWLClass_6fa705db_1014_4bbe_9e37_32983237e8d4 CVAO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/1163005009 SNOMEDCT LOOM
http://purl.obolibrary.org/obo/OMIM_236000 CCO LOOM
urn:agi-folder:hodgkin_lymphoma BPT LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0019829 MEDLINEPLUS LOOM