loading...| Preferred Name |
Granulomatosis with polyangiitis |
|
| Synonyms |
GPA |
|
| Definitions |
A rare anti-neutrophil cytoplasmic antibodies (ANCA)-associated vasculitis characterized by necrotizing inflammation of small and medium vessels (capillaries, venules and arterioles), resulting in tissue ischemia. |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_900 |
|
| alternative_term |
GPA |
|
| definition |
A rare anti-neutrophil cytoplasmic antibodies (ANCA)-associated vasculitis characterized by necrotizing inflammation of small and medium vessels (capillaries, venules and arterioles), resulting in tissue ischemia. |
|
| definition_citation |
Orphanet |
|
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=900 |
|
| has_age_of_onset |
Adolescent Adult Childhood Elderly |
|
| has_inheritance |
Not applicable |
|
| hasDbXref |
MeSH:D014890 MedDRA:10072579 UMLS:C3495801 ICD-11:4A44.A1 OMIM:608710 ICD-10:M31.3 |
|
| label |
Granulomatosis with polyangiitis |
|
| notation |
ORPHA:900 |
|
| part_of |
http://www.orpha.net/ORDO/Orphanet_567560 http://www.orpha.net/ORDO/Orphanet_156152 |
|
| prefixIRI |
ORDO:Orphanet_900 |
|
| prefLabel |
Granulomatosis with polyangiitis |
|
| present_in |
Italy AND has_point_prevalence_average_value : 3.43 AND has_point_prevalence_range : 1-9 / 100 000 Japan AND has_annual_incidence_average_value : 0.21 AND has_annual_incidence_range : 1-9 / 1 000 000 Spain AND has_annual_incidence_average_value : 0.49 AND has_annual_incidence_range : 1-9 / 1 000 000 Japan AND has_point_prevalence_average_value : 0.23 AND has_point_prevalence_range : 1-9 / 1 000 000 Canada AND has_annual_incidence_average_value : 0.46 AND has_annual_incidence_range : 1-9 / 1 000 000 Greece AND has_annual_incidence_average_value : 0.66 AND has_annual_incidence_range : 1-9 / 1 000 000 New Zealand AND has_point_prevalence_average_value : 9.35 AND has_point_prevalence_range : 1-9 / 100 000 Norway AND has_annual_incidence_average_value : 1.0 AND has_annual_incidence_range : 1-9 / 100 000 Taiwan, Province of China AND has_annual_incidence_average_value : 0.037 AND has_annual_incidence_range : <1 / 1 000 000 United States AND has_point_prevalence_average_value : 2.6 AND has_point_prevalence_range : 1-9 / 100 000 Sweden AND has_annual_incidence_average_value : 1.19 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_annual_incidence_average_value : 0.85 AND has_annual_incidence_range : 1-9 / 1 000 000 Denmark AND has_point_prevalence_average_value : 10.0 AND has_point_prevalence_range : 1-5 / 10 000 Norway AND has_point_prevalence_average_value : 9.51 AND has_point_prevalence_range : 1-9 / 100 000 United States AND has_annual_incidence_average_value : 1.3 AND has_annual_incidence_range : 1-9 / 100 000 Finland AND has_annual_incidence_average_value : 0.93 AND has_annual_incidence_range : 1-9 / 1 000 000 China AND has_point_prevalence_average_value : 1.94 AND has_point_prevalence_range : 1-9 / 100 000 France AND has_point_prevalence_average_value : 2.37 AND has_point_prevalence_range : 1-9 / 100 000 United Kingdom AND has_annual_incidence_average_value : 1.0 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_point_prevalence_average_value : 9.0 AND has_point_prevalence_range : 1-9 / 100 000 Italy AND has_annual_incidence_average_value : 0.24 AND has_annual_incidence_range : 1-9 / 1 000 000 Australia AND has_point_prevalence_average_value : 9.5 AND has_point_prevalence_range : 1-9 / 100 000 Sweden AND has_point_prevalence_average_value : 16.0 AND has_point_prevalence_range : 1-5 / 10 000 Germany AND has_annual_incidence_average_value : 0.86 AND has_annual_incidence_range : 1-9 / 1 000 000 Lithuania AND has_annual_incidence_average_value : 0.21 AND has_annual_incidence_range : 1-9 / 1 000 000 |
|
| treeView |
http://www.orpha.net/ORDO/Orphanet_567560 http://www.orpha.net/ORDO/Orphanet_156152 |
|
| subClassOf |