loading...| Preferred Name |
Hepatic veno-occlusive disease |
|
| Synonyms |
Sinusoidal obstruction syndrome |
|
| Definitions |
A rare vascular liver disease characterized by toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins and sinusoids. Clinical manifestations include painful hepatomegaly, jaundice, and fluid retention that manifests by weight gain, edemas, and ascites. |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_890 |
|
| alternative_term |
Sinusoidal obstruction syndrome |
|
| definition |
A rare vascular liver disease characterized by toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins and sinusoids. Clinical manifestations include painful hepatomegaly, jaundice, and fluid retention that manifests by weight gain, edemas, and ascites. |
|
| definition_citation |
Orphanet |
|
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=890 |
|
| has_age_of_onset |
All ages |
|
| has_inheritance |
Not applicable |
|
| hasDbXref |
MeSH:D006504 UMLS:C0019156 MedDRA:10047216 ICD-10:K76.5 ICD-11:DB98.6 |
|
| label |
Hepatic veno-occlusive disease |
|
| notation |
ORPHA:890 |
|
| part_of | ||
| prefixIRI |
ORDO:Orphanet_890 |
|
| prefLabel |
Hepatic veno-occlusive disease |
|
| present_in |
Worldwide AND has_point_prevalence_range : Unknown |
|
| treeView | ||
| subClassOf |